{"id":6498,"date":"2023-04-18T19:15:20","date_gmt":"2023-04-18T19:15:20","guid":{"rendered":"https:\/\/restruct-lgmd-2021.pantheonsite.io\/?page_id=6498"},"modified":"2024-08-09T16:36:09","modified_gmt":"2024-08-09T16:36:09","slug":"all-about-lgmd","status":"publish","type":"page","link":"https:\/\/www.lgmd-info.org\/fr\/knowledge-base\/all-about-lgmd\/","title":{"rendered":"Tout savoir sur le LGMD"},"content":{"rendered":"<div class=\"fusion-fullwidth fullwidth-box fusion-builder-row-1 fusion-flex-container has-pattern-background has-mask-background nonhundred-percent-fullwidth non-hundred-percent-height-scrolling\" style=\"--awb-border-radius-top-left:0px;--awb-border-radius-top-right:0px;--awb-border-radius-bottom-right:0px;--awb-border-radius-bottom-left:0px;--awb-flex-wrap:wrap;\" ><div class=\"fusion-builder-row fusion-row fusion-flex-align-items-flex-start fusion-flex-content-wrap\" style=\"max-width:1456px;margin-left: calc(-4% \/ 2 );margin-right: calc(-4% \/ 2 );\"><div class=\"fusion-layout-column fusion_builder_column fusion-builder-column-0 fusion_builder_column_1_1 1_1 fusion-flex-column\" style=\"--awb-bg-size:cover;--awb-width-large:100%;--awb-margin-top-large:0px;--awb-spacing-right-large:1.92%;--awb-margin-bottom-large:20px;--awb-spacing-left-large:1.92%;--awb-width-medium:100%;--awb-order-medium:0;--awb-spacing-right-medium:1.92%;--awb-spacing-left-medium:1.92%;--awb-width-small:100%;--awb-order-small:0;--awb-spacing-right-small:1.92%;--awb-spacing-left-small:1.92%;\"><div class=\"fusion-column-wrapper fusion-column-has-shadow fusion-flex-justify-content-flex-start fusion-content-layout-column\"><div class=\"fusion-text fusion-text-1\"><p>Commencez \u00e0 comprendre la dystrophie musculaire des ceintures (DMG) gr\u00e2ce \u00e0 nos sections \"Aper\u00e7u et faits sur la DMG\" et \"Glossaire\". La section \"Vue d'ensemble et faits concernant la LGMD\" examine en profondeur les diff\u00e9rentes facettes de cette maladie, depuis ses d\u00e9finitions de base, ses influences g\u00e9n\u00e9tiques et l'\u00e9volution de ses sympt\u00f4mes jusqu'\u00e0 son impact quotidien et les derni\u00e8res avanc\u00e9es en mati\u00e8re de traitement et de recherche. Notre \"Glossaire\" est un guide de r\u00e9f\u00e9rence pratique qui clarifie les terminologies complexes et le vocabulaire sp\u00e9cialis\u00e9 utilis\u00e9s pour parler de la LGMD. Ensemble, ces ressources visent \u00e0 vous donner les moyens d'acqu\u00e9rir des connaissances et \u00e0 vous aider \u00e0 mieux comprendre cette maladie complexe.<\/p>\n<\/div><\/div><\/div><div class=\"fusion-layout-column fusion_builder_column fusion-builder-column-1 fusion_builder_column_1_3 1_3 fusion-flex-column fusion-column-inner-bg-wrapper fusion-column-liftup-border\" style=\"--awb-padding-top:15px;--awb-padding-right:15px;--awb-padding-bottom:5px;--awb-padding-left:15px;--awb-overflow:hidden;--awb-inner-bg-color:var(--awb-color2);--awb-inner-bg-color-hover:var(--awb-color2);--awb-inner-bg-blend:overlay;--awb-inner-bg-size:cover;--awb-inner-bg-box-shadow:0px 0px 1px 1px ;;--awb-border-radius:5px 5px 5px 5px;--awb-liftup-border-radius:5px 5px 5px 5px;--awb-width-large:33.333333333333%;--awb-margin-top-large:20px;--awb-spacing-right-large:5.76%;--awb-margin-bottom-large:20px;--awb-spacing-left-large:5.76%;--awb-width-medium:33.333333333333%;--awb-order-medium:0;--awb-spacing-right-medium:5.76%;--awb-spacing-left-medium:5.76%;--awb-width-small:100%;--awb-order-small:0;--awb-spacing-right-small:1.92%;--awb-spacing-left-small:1.92%;\"><span class=\"fusion-column-inner-bg hover-type-liftup\"><a class=\"fusion-column-anchor\" href=\"\/fr\/knowledge-base\/all-about-lgmd\/what-is-lgmd\/\"><span class=\"fusion-column-inner-bg-image\"><\/span><\/a><\/span><div class=\"fusion-column-wrapper fusion-flex-justify-content-flex-start fusion-content-layout-column\"><div class=\"fusion-builder-row fusion-builder-row-inner fusion-row fusion-flex-align-items-flex-start fusion-flex-content-wrap\" style=\"width:104% !important;max-width:104% !important;margin-left: calc(-4% \/ 2 );margin-right: calc(-4% \/ 2 );\"><div class=\"fusion-layout-column fusion_builder_column_inner fusion-builder-nested-column-0 fusion_builder_column_inner_3_4 3_4 fusion-flex-column\" style=\"--awb-bg-size:cover;--awb-width-large:75%;--awb-margin-top-large:0px;--awb-spacing-right-large:2.56%;--awb-margin-bottom-large:0px;--awb-spacing-left-large:2.56%;--awb-width-medium:75%;--awb-order-medium:0;--awb-spacing-right-medium:2.56%;--awb-spacing-left-medium:2.56%;--awb-width-small:75%;--awb-order-small:0;--awb-spacing-right-small:2.56%;--awb-spacing-left-small:2.56%;\"><div class=\"fusion-column-wrapper fusion-column-has-shadow fusion-flex-justify-content-flex-start fusion-content-layout-column\"><div class=\"fusion-title title fusion-title-1 fusion-sep-none fusion-title-text fusion-title-size-two\" style=\"--awb-text-color:var(--awb-color5);--awb-margin-bottom:5px;--awb-font-size:var(--awb-custom_typography_1-font-size);\"><h2 class=\"fusion-title-heading title-heading-left fusion-responsive-typography-calculated\" style=\"font-family:var(--awb-custom_typography_1-font-family);font-weight:var(--awb-custom_typography_1-font-weight);font-style:var(--awb-custom_typography_1-font-style);margin:0;font-size:1em;letter-spacing:var(--awb-custom_typography_1-letter-spacing);text-transform:var(--awb-custom_typography_1-text-transform);--fontSize:16;--minFontSize:16;line-height:var(--awb-custom_typography_1-line-height);\">LGMD : vue d'ensemble et faits<\/h2><\/div><\/div><\/div><div class=\"fusion-layout-column fusion_builder_column_inner fusion-builder-nested-column-1 fusion_builder_column_inner_1_4 1_4 fusion-flex-column\" style=\"--awb-bg-size:cover;--awb-width-large:25%;--awb-margin-top-large:0px;--awb-spacing-right-large:7.68%;--awb-margin-bottom-large:0px;--awb-spacing-left-large:7.68%;--awb-width-medium:25%;--awb-order-medium:0;--awb-spacing-right-medium:7.68%;--awb-spacing-left-medium:7.68%;--awb-width-small:25%;--awb-order-small:0;--awb-spacing-right-small:7.68%;--awb-spacing-left-small:7.68%;\"><div class=\"fusion-column-wrapper fusion-column-has-shadow fusion-flex-justify-content-flex-start fusion-content-layout-column\"><i class=\"fb-icon-element-1 fb-icon-element fontawesome-icon fa-angle-right fas circle-no\" style=\"--awb-iconcolor:var(--awb-color5);--awb-iconcolor-hover:var(--awb-color4);--awb-font-size:26px;--awb-align-self:flex-end;--awb-margin-top:5px;--awb-margin-right:15px;--awb-margin-bottom:5px;--awb-margin-left:0px;\"><\/i><\/div><\/div><\/div><div class=\"fusion-separator fusion-full-width-sep\" style=\"align-self: center;margin-left: auto;margin-right: auto;margin-top:5px;margin-bottom:5px;width:100%;\"><div class=\"fusion-separator-border sep-single\" style=\"--awb-height:20px;--awb-amount:20px;--awb-sep-color:var(--awb-color1);border-color:var(--awb-color1);border-top-width:1px;\"><\/div><\/div><div class=\"fusion-text fusion-text-2\"><p>D\u00e9couvrez tout, des d\u00e9finitions de base aux influences g\u00e9n\u00e9tiques, en passant par l'\u00e9volution des sympt\u00f4mes, l'impact quotidien et les derni\u00e8res avanc\u00e9es en mati\u00e8re de traitement et de recherche.<\/p>\n<\/div><\/div><\/div><div class=\"fusion-layout-column fusion_builder_column fusion-builder-column-2 fusion_builder_column_1_3 1_3 fusion-flex-column fusion-column-inner-bg-wrapper fusion-column-liftup-border\" style=\"--awb-padding-top:15px;--awb-padding-right:15px;--awb-padding-bottom:5px;--awb-padding-left:15px;--awb-overflow:hidden;--awb-inner-bg-color:var(--awb-color2);--awb-inner-bg-color-hover:var(--awb-color2);--awb-inner-bg-blend:overlay;--awb-inner-bg-size:cover;--awb-inner-bg-box-shadow:0px 0px 1px 1px ;;--awb-border-radius:5px 5px 5px 5px;--awb-liftup-border-radius:5px 5px 5px 5px;--awb-width-large:33.333333333333%;--awb-margin-top-large:20px;--awb-spacing-right-large:5.76%;--awb-margin-bottom-large:20px;--awb-spacing-left-large:5.76%;--awb-width-medium:33.333333333333%;--awb-order-medium:0;--awb-spacing-right-medium:5.76%;--awb-spacing-left-medium:5.76%;--awb-width-small:100%;--awb-order-small:0;--awb-spacing-right-small:1.92%;--awb-spacing-left-small:1.92%;\"><span class=\"fusion-column-inner-bg hover-type-liftup\"><a class=\"fusion-column-anchor\" href=\"\/fr\/knowledge-base\/all-about-lgmd\/glossary\/\"><span class=\"fusion-column-inner-bg-image\"><\/span><\/a><\/span><div class=\"fusion-column-wrapper fusion-flex-justify-content-flex-start fusion-content-layout-column\"><div class=\"fusion-builder-row fusion-builder-row-inner fusion-row fusion-flex-align-items-flex-start fusion-flex-content-wrap\" style=\"width:104% !important;max-width:104% !important;margin-left: calc(-4% \/ 2 );margin-right: calc(-4% \/ 2 );\"><div class=\"fusion-layout-column fusion_builder_column_inner fusion-builder-nested-column-2 fusion_builder_column_inner_3_4 3_4 fusion-flex-column\" style=\"--awb-bg-size:cover;--awb-width-large:75%;--awb-margin-top-large:0px;--awb-spacing-right-large:2.56%;--awb-margin-bottom-large:0px;--awb-spacing-left-large:2.56%;--awb-width-medium:75%;--awb-order-medium:0;--awb-spacing-right-medium:2.56%;--awb-spacing-left-medium:2.56%;--awb-width-small:75%;--awb-order-small:0;--awb-spacing-right-small:2.56%;--awb-spacing-left-small:2.56%;\"><div class=\"fusion-column-wrapper fusion-column-has-shadow fusion-flex-justify-content-flex-start fusion-content-layout-column\"><div class=\"fusion-title title fusion-title-2 fusion-sep-none fusion-title-text fusion-title-size-two\" style=\"--awb-text-color:var(--awb-color5);--awb-margin-bottom:5px;--awb-font-size:var(--awb-custom_typography_1-font-size);\"><h2 class=\"fusion-title-heading title-heading-left fusion-responsive-typography-calculated\" style=\"font-family:var(--awb-custom_typography_1-font-family);font-weight:var(--awb-custom_typography_1-font-weight);font-style:var(--awb-custom_typography_1-font-style);margin:0;font-size:1em;letter-spacing:var(--awb-custom_typography_1-letter-spacing);text-transform:var(--awb-custom_typography_1-text-transform);--fontSize:16;--minFontSize:16;line-height:var(--awb-custom_typography_1-line-height);\">Glossaire<\/h2><\/div><\/div><\/div><div class=\"fusion-layout-column fusion_builder_column_inner fusion-builder-nested-column-3 fusion_builder_column_inner_1_4 1_4 fusion-flex-column\" style=\"--awb-bg-size:cover;--awb-width-large:25%;--awb-margin-top-large:0px;--awb-spacing-right-large:7.68%;--awb-margin-bottom-large:0px;--awb-spacing-left-large:7.68%;--awb-width-medium:25%;--awb-order-medium:0;--awb-spacing-right-medium:7.68%;--awb-spacing-left-medium:7.68%;--awb-width-small:25%;--awb-order-small:0;--awb-spacing-right-small:7.68%;--awb-spacing-left-small:7.68%;\"><div class=\"fusion-column-wrapper fusion-column-has-shadow fusion-flex-justify-content-flex-start fusion-content-layout-column\"><i class=\"fb-icon-element-2 fb-icon-element fontawesome-icon fa-angle-right fas circle-no\" style=\"--awb-iconcolor:var(--awb-color5);--awb-iconcolor-hover:var(--awb-color4);--awb-font-size:26px;--awb-align-self:flex-end;--awb-margin-top:5px;--awb-margin-right:15px;--awb-margin-bottom:5px;--awb-margin-left:0px;\"><\/i><\/div><\/div><\/div><div class=\"fusion-separator fusion-full-width-sep\" style=\"align-self: center;margin-left: auto;margin-right: auto;margin-top:5px;margin-bottom:5px;width:100%;\"><div class=\"fusion-separator-border sep-single\" style=\"--awb-height:20px;--awb-amount:20px;--awb-sep-color:var(--awb-color1);border-color:var(--awb-color1);border-top-width:1px;\"><\/div><\/div><div class=\"fusion-text fusion-text-3\"><p>Se familiariser avec le vocabulaire sp\u00e9cialis\u00e9 et les terminologies complexes utilis\u00e9s pour comprendre et discuter de la dystrophie musculaire des ceintures.<\/p>\n<\/div><\/div><\/div><div class=\"fusion-layout-column fusion_builder_column fusion-builder-column-3 fusion_builder_column_1_3 1_3 fusion-flex-column fusion-column-inner-bg-wrapper fusion-column-liftup-border\" style=\"--awb-padding-top:15px;--awb-padding-right:15px;--awb-padding-bottom:5px;--awb-padding-left:15px;--awb-overflow:hidden;--awb-inner-bg-color:var(--awb-color2);--awb-inner-bg-color-hover:var(--awb-color2);--awb-inner-bg-blend:overlay;--awb-inner-bg-size:cover;--awb-inner-bg-box-shadow:0px 0px 1px 1px ;;--awb-border-radius:5px 5px 5px 5px;--awb-liftup-border-radius:5px 5px 5px 5px;--awb-width-large:33.333333333333%;--awb-margin-top-large:20px;--awb-spacing-right-large:5.76%;--awb-margin-bottom-large:20px;--awb-spacing-left-large:5.76%;--awb-width-medium:33.333333333333%;--awb-order-medium:0;--awb-spacing-right-medium:5.76%;--awb-spacing-left-medium:5.76%;--awb-width-small:100%;--awb-order-small:0;--awb-spacing-right-small:1.92%;--awb-spacing-left-small:1.92%;\" data-scroll-devices=\"small-visibility,medium-visibility,large-visibility\"><span class=\"fusion-column-inner-bg hover-type-liftup\"><a class=\"fusion-column-anchor\" href=\"\/fr\/knowledge-base\/lgmd-milestones-a-decade-of-difference\/\"><span class=\"fusion-column-inner-bg-image\"><\/span><\/a><\/span><div class=\"fusion-column-wrapper fusion-flex-justify-content-flex-start fusion-content-layout-column\"><div class=\"fusion-builder-row fusion-builder-row-inner fusion-row fusion-flex-align-items-flex-start fusion-flex-content-wrap\" style=\"width:104% !important;max-width:104% !important;margin-left: calc(-4% \/ 2 );margin-right: calc(-4% \/ 2 );\"><div class=\"fusion-layout-column fusion_builder_column_inner fusion-builder-nested-column-4 fusion_builder_column_inner_3_4 3_4 fusion-flex-column\" style=\"--awb-bg-size:cover;--awb-width-large:75%;--awb-margin-top-large:0px;--awb-spacing-right-large:2.56%;--awb-margin-bottom-large:0px;--awb-spacing-left-large:2.56%;--awb-width-medium:75%;--awb-order-medium:0;--awb-spacing-right-medium:2.56%;--awb-spacing-left-medium:2.56%;--awb-width-small:75%;--awb-order-small:0;--awb-spacing-right-small:2.56%;--awb-spacing-left-small:2.56%;\"><div class=\"fusion-column-wrapper fusion-column-has-shadow fusion-flex-justify-content-flex-start fusion-content-layout-column\"><div class=\"fusion-title title fusion-title-3 fusion-sep-none fusion-title-text fusion-title-size-two\" style=\"--awb-text-color:var(--awb-color5);--awb-margin-bottom:5px;--awb-font-size:var(--awb-custom_typography_1-font-size);\"><h2 class=\"fusion-title-heading title-heading-left fusion-responsive-typography-calculated\" style=\"font-family:var(--awb-custom_typography_1-font-family);font-weight:var(--awb-custom_typography_1-font-weight);font-style:var(--awb-custom_typography_1-font-style);margin:0;font-size:1em;letter-spacing:var(--awb-custom_typography_1-letter-spacing);text-transform:var(--awb-custom_typography_1-text-transform);--fontSize:16;--minFontSize:16;line-height:var(--awb-custom_typography_1-line-height);\">Jalons du LGMD<\/h2><\/div><\/div><\/div><div class=\"fusion-layout-column fusion_builder_column_inner fusion-builder-nested-column-5 fusion_builder_column_inner_1_4 1_4 fusion-flex-column\" style=\"--awb-bg-size:cover;--awb-width-large:25%;--awb-margin-top-large:0px;--awb-spacing-right-large:7.68%;--awb-margin-bottom-large:0px;--awb-spacing-left-large:7.68%;--awb-width-medium:25%;--awb-order-medium:0;--awb-spacing-right-medium:7.68%;--awb-spacing-left-medium:7.68%;--awb-width-small:25%;--awb-order-small:0;--awb-spacing-right-small:7.68%;--awb-spacing-left-small:7.68%;\"><div class=\"fusion-column-wrapper fusion-column-has-shadow fusion-flex-justify-content-flex-start fusion-content-layout-column\"><i class=\"fb-icon-element-3 fb-icon-element fontawesome-icon fa-angle-right fas circle-no\" style=\"--awb-iconcolor:var(--awb-color5);--awb-iconcolor-hover:var(--awb-color4);--awb-font-size:26px;--awb-align-self:flex-end;--awb-margin-top:5px;--awb-margin-right:15px;--awb-margin-bottom:5px;--awb-margin-left:0px;\"><\/i><\/div><\/div><\/div><div class=\"fusion-separator fusion-full-width-sep\" style=\"align-self: center;margin-left: auto;margin-right: auto;margin-top:5px;margin-bottom:5px;width:100%;\"><div class=\"fusion-separator-border sep-single\" style=\"--awb-height:20px;--awb-amount:20px;--awb-sep-color:var(--awb-color1);border-color:var(--awb-color1);border-top-width:1px;\"><\/div><\/div><div class=\"fusion-text fusion-text-4\"><p>D\u00e9couvrez une d\u00e9cennie d'\u00e9v\u00e9nements marquants dans la lutte contre la dystrophie musculaire des ceintures (LGMD).<\/p>\n<\/div><\/div><\/div><\/div><\/div>","protected":false},"excerpt":{"rendered":"","protected":false},"author":1,"featured_media":0,"parent":43,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","meta":{"_acf_changed":false,"footnotes":""},"class_list":["post-6498","page","type-page","status-publish","hentry"],"acf":[],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v23.9 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>All About LGMD - LGMD Awareness Foundation<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/www.lgmd-info.org\/fr\/knowledge-base\/all-about-lgmd\/\" \/>\n<meta property=\"og:locale\" content=\"fr_FR\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"All About LGMD - LGMD Awareness Foundation\" \/>\n<meta property=\"og:url\" content=\"https:\/\/www.lgmd-info.org\/fr\/knowledge-base\/all-about-lgmd\/\" \/>\n<meta property=\"og:site_name\" content=\"LGMD Awareness Foundation\" \/>\n<meta property=\"article:publisher\" content=\"https:\/\/www.facebook.com\/LGMDawareness\/\" \/>\n<meta property=\"article:modified_time\" content=\"2024-08-09T16:36:09+00:00\" \/>\n<meta property=\"og:image\" content=\"https:\/\/www.lgmd-info.org\/wp-content\/uploads\/2021\/06\/LGMD-Logo_1200X630.png\" \/>\n\t<meta property=\"og:image:width\" content=\"1200\" \/>\n\t<meta property=\"og:image:height\" content=\"630\" 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