{"id":2862,"date":"2019-10-01T20:27:15","date_gmt":"2019-10-02T01:27:15","guid":{"rendered":"https:\/\/restruct-lgmd-2021.pantheonsite.io\/?p=2862"},"modified":"2019-10-01T20:27:15","modified_gmt":"2019-10-02T01:27:15","slug":"william","status":"publish","type":"post","link":"https:\/\/www.lgmd-info.org\/ja\/individuals-with-lgmd-interviews\/2019\/10\/01\/william\/","title":{"rendered":"LGMD\u500b\u4eba\uff1a\u30a6\u30a3\u30ea\u30a2\u30e0"},"content":{"rendered":"<figure class=\"wp-block-image\"><img decoding=\"async\" src=\"data:image\/svg+xml,%3Csvg%20xmlns%3D%27http%3A%2F%2Fwww.w3.org%2F2000%2Fsvg%27%20width%3D%271024%27%20height%3D%27576%27%20viewBox%3D%270%200%201024%20576%27%3E%3Crect%20width%3D%271024%27%20height%3D%27576%27%20fill-opacity%3D%220%22%2F%3E%3C%2Fsvg%3E\" data-orig-src=\"https:\/\/www.lgmd-info.org\/wp-content\/uploads\/2019\/10\/LGMD1D-William-1024x576.png\" alt=\"\" class=\"lazyload wp-image-2860\"\/><\/figure>\n\n\n\n<p><strong>LGMD \"\u30b9\u30dd\u30c3\u30c8\u30e9\u30a4\u30c8\u30fb\u30a4\u30f3\u30bf\u30d3\u30e5\u30fc\"<\/strong><\/p>\n\n\n\n<p><strong>\u540d\u79f0<\/strong>:  \u30a6\u30a3\u30ea\u30a2\u30e0&nbsp;\n<strong>\u5e74\u9f62<\/strong>:\n62\u6b73<\/p>\n\n\n\n<p><strong>\u56fd\u540d<\/strong>:\u30a2\u30e1\u30ea\u30ab<\/p>\n\n\n\n<p><strong>LGMD\u30b5\u30d6\u30bf\u30a4\u30d7<\/strong>:   LGMD D1 DNAJB6\u95a2\u9023\uff08\u65e7LGMD 1D\u578b\uff09<\/p>\n\n\n\n<p><strong>\u4f55\u6b73\u3067\u8a3a\u65ad\u3092\u53d7\u3051\u305f\u304b<\/strong>:<\/p>\n\n\n\n<p>\u79c1\u306f40\u6b73\u306e\u3068\u304d\u306b\u81e8\u5e8a\u8a3a\u65ad\u3092\u53d7\u3051\u30015\u5e74\u5f8c\u306e45\u6b73\u306e\u3068\u304d\u306bLGMD 1D\u3067\u3042\u308b\u3053\u3068\u304c\u907a\u4f1d\u5b50\u5b66\u7684\u306b\u78ba\u8a8d\u3055\u308c\u305f\u3002<\/p>\n\n\n\n<p><strong>\u6700\u521d\u306e\u75c7\u72b6\u306f\uff1f<\/strong>:<\/p>\n\n\n\n<p>\u5b50\u4f9b\u306e\u9803\u3001\u79c1\u306f\u8db3\u304c\u9045\u304b\u3063\u305f\u3002  45\u6b73\u306e\u9803\u3001\u8d70\u308b\u306e\u304c\u56f0\u96e3\u306b\u306a\u3063\u305f\u3002<\/p>\n\n\n\n<p><strong>\u3054\u5bb6\u65cf\u306bLGMD\u306e\u65b9\u306f\u3044\u3089\u3063\u3057\u3083\u3044\u307e\u3059\u304b\uff1f<\/strong><\/p>\n\n\n\n<p>\u3048\u3048\u300167\u6b73\u306e\u5144\u304cLGMD1D\u3067\u3001\u5a18\u3082\u305d\u3046\u3067\u3059\u3002\n\u5a18\u3082\u305d\u3046\u3067\u3059\u3002<\/p>\n\n\n\n<p><strong>LGMD\u3068\u5171\u306b\u751f\u304d\u3066\u3044\u304f\u4e0a\u3067\nLGMD\u3068\u5171\u306b\u751f\u304d\u308b\u4e0a\u3067<\/strong>:<\/p>\n\n\n\n<p>\u79c1\u306b\u3068\u3063\u3066\u306e\u6700\u5927\u306e\u6311\u6226\u306f\u3001\u8870\u3048\u306b\u9069\u5fdc\u3059\u308b\u3053\u3068\u3060\u3063\u305f\u3002\n\u5f90\u3005\u306b\u30da\u30fc\u30b9\u3092\u843d\u3068\u3055\u306a\u3051\u308c\u3070\u306a\u3089\u306a\u3044\u3053\u3068\u3060\u3002<\/p>\n\n\n\n<p><strong>\u3042\u306a\u305f\u306e\u6700\u5927\u306e\u529f\u7e3e\u306f\u4f55\u3067\u3059\u304b\uff1f<\/strong>:<\/p>\n\n\n\n<p>\u79c1\u306e\u6700\u5927\u306e\u529f\u7e3e\u306f\u3001LGMD-1D\u8ca1\u56e3\u3092\u7acb\u3061\u4e0a\u3052\u305f\u3053\u3068\u3067\u3059\u3002\nDNAJB6\u8ca1\u56e3\u3092\u8a2d\u7acb\u3057\u305f\u3053\u3068\u3067\u3042\u308b\u3002\n\u305d\u306e\u4f7f\u547d\u306f\u3001\u80a2\u5e2f\u7b4b\u30b8\u30b9\u30c8\u30ed\u30d5\u30a3\u30fc1\u578b\uff08LGMD1D\uff09\u3068\u8a3a\u65ad\u3055\u308c\u305f\u4eba\u305f\u3061\u304c\n\u305d\u306e\u4f7f\u547d\u306f\u3001\u80a2\u5e2f\u578b\u7b4b\u30b8\u30b9\u30c8\u30ed\u30d5\u30a3\u30fc1D\uff08LGMD1D\uff09\u3068\u8a3a\u65ad\u3055\u308c\u305f\u4eba\u3005\u304c\u96c6\u307e\u308a\u3001\u95a2\u9023\u30cb\u30e5\u30fc\u30b9\u3092\u96c6\u7d04\u3057\u3001\u52df\u91d1\u6d3b\u52d5\u3092\u958b\u59cb\u3059\u308b\u305f\u3081\u306e\u4e2d\u5fc3\u7684\u306a\u5834\u6240\u3092\u7dad\u6301\u3059\u308b\u3053\u3068\u3067\u3042\u308b\u3002\n\u52df\u91d1\u6d3b\u52d5\u3092\u884c\u3046\u305f\u3081\u306e\u4e2d\u5fc3\u7684\u306a\u5834\u6240\u3092\u7dad\u6301\u3059\u308b\u3053\u3068\u3092\u4f7f\u547d\u3068\u3057\u3066\u3044\u307e\u3059\u3002&nbsp; <a href=\"https:\/\/lgmd1d.org\">https:\/\/lgmd1d.org<\/a>\n<\/p>\n\n\n\n<p>\u307e\u305f\u3001\u5e38\u67d3\u8272\u4f53\u512a\u6027\u907a\u4f1d\u306eLGMD\u3068\u8a3a\u65ad\u3055\u308c\u305f\u3059\u3079\u3066\u306e\u60a3\u8005\u306e\u305f\u3081\u306e\u60a3\u8005\u767b\u9332\u3082\u884c\u3063\u3066\u3044\u307e\u3059\u3002  (LGMD1\u578b\uff09<\/p>\n\n\n\n<p><strong>LGMD\u306f\u3042\u306a\u305f\u306b\u3069\u306e\u3088\u3046\u306a\u5f71\u97ff\u3092\u4e0e\u3048\u307e\u3057\u305f\u304b\uff1f\n\u4eca\u306e\u3042\u306a\u305f\u306b\u3069\u306e\u3088\u3046\u306a\u5f71\u97ff\u3092\u4e0e\u3048\u3066\u3044\u307e\u3059\u304b\uff1f<\/strong><\/p>\n\n\n\n<p>LGMD\u306f\u79c1\u306e\u4eba\u751f\u3068\u4eca\u65e5\u306e\u79c1\u306b\u5f71\u97ff\u3092\u4e0e\u3048\u305f\u3002  \u30b9\u30ed\u30fc\u30c0\u30a6\u30f3\u3059\u308b\u3053\u3068\u3067\n\u5bb6\u65cf\u3001\u53cb\u4eba\u3001\u305d\u3057\u3066\u3064\u306a\u304c\u308a\u3002<\/p>\n\n\n\n<p><strong>LGMD\u306b\u3064\u3044\u3066\u4e16\u754c\u306b\u77e5\u3063\u3066\u3082\u3089\u3044\u305f\u3044\u3053\u3068\u306f\uff1f<\/strong>:<\/p>\n\n\n\n<p>\u79c1\u305f\u3061\u306f\u3001\u3053\u306e\u8a00\u8449\u3092\u5e83\u3081\u3001\u6cbb\u7642\u306b\u5f79\u7acb\u3064\u65b9\u6cd5\u3067\u3064\u306a\u304c\u308a\u7d9a\u3051\u308b\u5fc5\u8981\u304c\u3042\u308a\u307e\u3059\u3002  \u4f8b\u3048\u3070\u3001\u5e38\u67d3\u8272\u4f53\u512a\u6027\u907a\u4f1dLGMD\uff08LGMD1\u578b\uff09\u306e\u60a3\u8005\u767b\u9332\u306f\u3001\u7814\u7a76\u3068\u6cbb\u7642\u6cd5\u306e\u767a\u898b\u306b\u4e0d\u53ef\u6b20\u3067\u3059\u3002<\/p>\n\n\n\n<p><strong>\u3082\u3057\u660e\u65e5\u3001\u3042\u306a\u305f\u306eLGMD\u304c \"\u6cbb\u308b \"\u3068\u3057\u305f\u3089\u3001\u307e\u305a\u4f55\u3092\u3057\u305f\u3044\u3067\u3059\u304b\uff1f\n\u307e\u305a\u4f55\u3092\u3057\u305f\u3044\u3067\u3059\u304b\uff1f<\/strong>:<\/p>\n\n\n\n<p>\u3082\u3057\u660e\u65e5\u6cbb\u3063\u305f\u3089\u3001\u30c0\u30f3\u30b9\u306b\u884c\u3063\u305f\u308a\u3001\u5b6b\u5a18\u305f\u3061\u3068\u30b5\u30c3\u30ab\u30fc\u3092\u3057\u305f\u308a\u3059\u308b\u3088<\/p>\n\n\n\n<p> <\/p>","protected":false},"excerpt":{"rendered":"<p>LGMD \u201cSpotlight interview\u201d Name:&nbsp; William&nbsp; Age: 62 years old Country: [&hellip;]<\/p>","protected":false},"author":1,"featured_media":2860,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"_acf_changed":false,"footnotes":""},"categories":[13,102,104],"tags":[103],"class_list":["post-2862","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-individuals-with-lgmd-interviews","category-lgmd-d1-dnajb6-related","category-lgmd1d","tag-lgmd-d1-dnajb6-related-united-states-lgmd1d"],"acf":[],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v23.9 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>Individual with LGMD: William - LGMD Awareness Foundation<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/www.lgmd-info.org\/ja\/individuals-with-lgmd-interviews\/2019\/10\/01\/william\/\" \/>\n<meta property=\"og:locale\" content=\"ja_JP\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Individual with LGMD: William - LGMD Awareness Foundation\" \/>\n<meta property=\"og:description\" content=\"LGMD \u201cSpotlight interview\u201d Name:&nbsp; 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