{"id":5635,"date":"2022-02-08T04:21:00","date_gmt":"2022-02-08T04:21:00","guid":{"rendered":"https:\/\/www.lgmd-info.org\/?p=5635"},"modified":"2024-02-09T14:23:56","modified_gmt":"2024-02-09T14:23:56","slug":"individual-with-lgmd-john","status":"publish","type":"post","link":"https:\/\/www.lgmd-info.org\/ja\/individuals-with-lgmd-interviews\/2022\/02\/08\/individual-with-lgmd-john\/","title":{"rendered":"LGMD\u60a3\u8005\uff1a\u30b8\u30e7\u30f3"},"content":{"rendered":"<div class=\"fusion-fullwidth fullwidth-box fusion-builder-row-1 fusion-flex-container has-pattern-background has-mask-background hundred-percent-fullwidth non-hundred-percent-height-scrolling\" style=\"--awb-border-radius-top-left:0px;--awb-border-radius-top-right:0px;--awb-border-radius-bottom-right:0px;--awb-border-radius-bottom-left:0px;--awb-flex-wrap:wrap;\" ><div class=\"fusion-builder-row fusion-row fusion-flex-align-items-flex-start fusion-flex-content-wrap\" style=\"width:104% !important;max-width:104% 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width=\"300\" height=\"169\" srcset=\"data:image\/svg+xml,%3Csvg%20xmlns%3D%27http%3A%2F%2Fwww.w3.org%2F2000%2Fsvg%27%20width%3D%27300%27%20height%3D%27169%27%20viewBox%3D%270%200%20300%20169%27%3E%3Crect%20width%3D%27300%27%20height%3D%27169%27%20fill-opacity%3D%220%22%2F%3E%3C%2Fsvg%3E\" data-srcset=\"https:\/\/www.lgmd-info.org\/wp-content\/uploads\/2022\/02\/LGMD2J-John-F-200x113.png 200w, https:\/\/www.lgmd-info.org\/wp-content\/uploads\/2022\/02\/LGMD2J-John-F-300x169.png 300w, https:\/\/www.lgmd-info.org\/wp-content\/uploads\/2022\/02\/LGMD2J-John-F-400x225.png 400w, https:\/\/www.lgmd-info.org\/wp-content\/uploads\/2022\/02\/LGMD2J-John-F-600x338.png 600w, https:\/\/www.lgmd-info.org\/wp-content\/uploads\/2022\/02\/LGMD2J-John-F-768x432.png 768w, https:\/\/www.lgmd-info.org\/wp-content\/uploads\/2022\/02\/LGMD2J-John-F-800x450.png 800w, https:\/\/www.lgmd-info.org\/wp-content\/uploads\/2022\/02\/LGMD2J-John-F-1024x576.png 1024w, https:\/\/www.lgmd-info.org\/wp-content\/uploads\/2022\/02\/LGMD2J-John-F-1200x675.png 1200w, https:\/\/www.lgmd-info.org\/wp-content\/uploads\/2022\/02\/LGMD2J-John-F.png 1280w\" data-sizes=\"auto\" data-orig-sizes=\"(max-width: 300px) 100vw, 300px\" \/><\/p>\n<p><strong>\u540d\u79f0<\/strong>:      \u30b8\u30e7\u30f3\u00a0\u00a0\u00a0\u00a0\u00a0\u00a0\u00a0\u00a0\u00a0\u00a0\u00a0\u00a0\u00a0\u00a0\u00a0\u00a0\u00a0 <strong>\u5e74\u9f62<\/strong>28\u6b73<\/p>\n<p><strong>\u56fd\u540d<\/strong>:   \u30a2\u30e1\u30ea\u30ab<\/p>\n<p><strong>LGMD\u30b5\u30d6\u30bf\u30a4\u30d7<\/strong>:    LGMD 2J\/R10 \u30bf\u30a4\u30c1\u30f3\u95a2\u9023<\/p>\n<p>&nbsp;<\/p>\n<p><strong>\u4f55\u6b73\u3067\u8a3a\u65ad\u3092\u53d7\u3051\u305f\u304b<\/strong>?<\/p>\n<p>10\u6b73\u306e\u3068\u304d\u3001\u79c1\u306f\u30d9\u30c3\u30ab\u30fc\u75c5\u3068\u8a3a\u65ad\u3055\u308c\u305f\u3002  11\u6b73\u304b12\u6b73\u306e\u9803\u3001\u30df\u30c8\u30b3\u30f3\u30c9\u30ea\u30a2\u30df\u30aa\u30d1\u30c1\u30fc\u3068\u8a3a\u65ad\u3055\u308c\u307e\u3057\u305f\u3002  2016\u5e74\u306bLGMD\u3068\u8a3a\u65ad\u3055\u308c\u30012021\u5e74\u306b\u3088\u3046\u3084\u304fLGMD2J\/R10\u304c\u907a\u4f1d\u5b66\u7684\u306b\u78ba\u5b9a\u3055\u308c\u307e\u3057\u305f\u3002<\/p>\n<p><strong>\u6700\u521d\u306e\u75c7\u72b6\u306f\u4f55\u3067\u3057\u305f\u304b\uff1f<\/strong><\/p>\n<p>5\u6b73\u3054\u308d\u304b\u3089\u3046\u307e\u304f\u6b69\u3051\u306a\u304f\u306a\u3063\u305f\u3002  \u904b\u52d5\u3059\u308b\u3068\u3075\u304f\u3089\u306f\u304e\u304c\u3068\u3066\u3064\u3082\u306a\u3044\u75db\u307f\u306b\u8972\u308f\u308c\u3001\u4ed6\u306e\u5b50\u306b\u3064\u3044\u3066\u3044\u304f\u306e\u3082\u5927\u5909\u3067\u3057\u305f\u3002<\/p>\n<p><strong>LGMD\u3092\u60a3\u3063\u3066\u3044\u308b\u5bb6\u65cf\u304c\u4ed6\u306b\u3044\u307e\u3059\u304b\uff1f<\/strong><\/p>\n<p>\u79c1\u306e\u5144\u3082LGMD2J\u3067\u3059\u3002<\/p>\n<p><strong>LGMD\u3068\u5171\u306b\u751f\u304d\u3066\u3044\u304f\u4e0a\u3067\u3001\u6700\u3082\u56f0\u96e3\u3060\u3068\u611f\u3058\u308b\u3053\u3068\u306f\u4f55\u3067\u3059\u304b\uff1f<\/strong>?<\/p>\n<p>\u6700\u5927\u306e\u8ab2\u984c\u306f\u3001\u597d\u304d\u306a\u3053\u3068\u304c\u3067\u304d\u306a\u304f\u306a\u308b\u3053\u3068\u3068\u3001\u8870\u5f31\u304c\u9032\u884c\u3057\u3066\u3044\u308b\u305f\u3081\u306b\u65b0\u3057\u3044\u8da3\u5473\u3092\u4f55\u5ea6\u3082\u898b\u3064\u3051\u306a\u3051\u308c\u3070\u306a\u3089\u306a\u3044\u3053\u3068\u3060\u3002  \u305d\u308c\u306b\u5bfe\u51e6\u3059\u308b\u306e\u306f\u96e3\u3057\u3044\u3002   \u307e\u305f\u3001\u7d20\u6674\u3089\u3057\u3044\u59bb\u30af\u30ea\u30b9\u30c6\u30a3\u30fc\u30ca\u306e\u52a9\u3051\u306a\u3057\u306b\u306f\u3001\u65e5\u5e38\u751f\u6d3b\u3092\u81ea\u7acb\u3057\u3066\u3053\u306a\u3059\u3053\u3068\u304c\u96e3\u3057\u3044\u3001\u3042\u308b\u3044\u306f\u4e0d\u53ef\u80fd\u3067\u3042\u308b\u3053\u3068\u3082\u5206\u304b\u3063\u3066\u304d\u305f\u3002\u6b8b\u5ff5\u306a\u3053\u3068\u306b\u3001\u79c1\u306e\u969c\u5bb3\u306e\u6027\u8cea\u3068\u4f7f\u7528\u3057\u3066\u3044\u308b\u79fb\u52d5\u5668\u5177\u306e\u305b\u3044\u3067\u3001\u79c1\u306f\u3057\u3070\u3057\u3070\u5dee\u5225\u3092\u53d7\u3051\u3001\u516c\u5171\u306e\u5834\u6240\u3078\u306e\u7acb\u3061\u5165\u308a\u3092\u62d2\u5426\u3055\u308c\u308b\u3053\u3068\u304c\u3042\u308b\u3002<\/p>\n<p><strong>\u3042\u306a\u305f\u306e\u6700\u5927\u306e\u529f\u7e3e\u306f\u4f55\u3067\u3059\u304b\uff1f<\/strong><\/p>\n<p>\u7f8e\u3057\u3044\u59bb\u30af\u30ea\u30b9\u30c6\u30a3\u30fc\u30ca\u3068\u7d50\u5a5a\u3057\u3001\u5316\u5b66\u306e\u5b66\u58eb\u53f7\u3092\u53d6\u5f97\u3002<\/p>\n<p><strong>LGMD\u306f\u4eca\u306e\u3042\u306a\u305f\u306b\u3069\u306e\u3088\u3046\u306a\u5f71\u97ff\u3092\u4e0e\u3048\u3066\u3044\u307e\u3059\u304b\uff1f<\/strong><\/p>\n<p>\u3053\u306e\u75c5\u6c17\u3092\u60a3\u3063\u305f\u3053\u3068\u3067\u3001\u30c1\u30e3\u30ec\u30f3\u30b8\u7cbe\u795e\u304c\u82bd\u751f\u3048\u3001\u969c\u5bb3\u8005\u30b3\u30df\u30e5\u30cb\u30c6\u30a3\u30fc\u306e\u4ed6\u306e\u4eba\u305f\u3061\u3068\u306e\u51fa\u4f1a\u3044\u304c\u3042\u308a\u3001\u4eca\u65e5\u306e\u3088\u3046\u306a\u64c1\u8b77\u8005\u306b\u306a\u308b\u3088\u3046\u80cc\u4e2d\u3092\u62bc\u3057\u3066\u304f\u308c\u305f\u3002  \u8eab\u4f53\u80fd\u529b\u304c\u5236\u9650\u3055\u308c\u3066\u3044\u308b\u3053\u3068\u3067\u3001\u79c1\u306f\u3088\u308a\u5275\u9020\u7684\u306a\u554f\u984c\u89e3\u6c7a\u8005\u306b\u306a\u308a\u3001\u5fcd\u8010\u306b\u3064\u3044\u3066\u591a\u304f\u306e\u3053\u3068\u3092\u5b66\u3073\u307e\u3057\u305f\u3002  \u75c5\u6c17\u306f\u672c\u5f53\u306b\u79c1\u3092\u6253\u3061\u306e\u3081\u3059\u3088\u3046\u306b\u611f\u3058\u308b\u3053\u3068\u304c\u3042\u308a\u307e\u3059\u304c\u3001\u79c1\u306e\u3088\u3046\u306a\u72b6\u614b\u306e\u771f\u306e\u6cbb\u7642\u3092\u6c42\u3081\u308b\u95d8\u3044\u306b\u304a\u3044\u3066\u3001\u79c1\u4e00\u4eba\u3067\u306f\u306a\u3044\u3053\u3068\u3092\u601d\u3044\u51fa\u3059\u3053\u3068\u306f\u91cd\u8981\u3067\u3059\u3002<\/p>\n<p><strong>LGMD\u306b\u3064\u3044\u3066\u4e16\u754c\u306b\u77e5\u3063\u3066\u3082\u3089\u3044\u305f\u3044\u3053\u3068\u306f\uff1f<\/strong>?<\/p>\n<p>LGMD\u306e\u3088\u3046\u306a\u75be\u60a3\u3092\u6301\u3064\u3053\u3068\u304c\u3001\u305d\u306e\u4eba\u306e\u4eba\u751f\u3001\u7cbe\u795e\u7684\u5065\u5eb7\u3001\u305d\u3057\u3066\u4eba\u751f\u306e\u671f\u5f85\u306b\u4e0e\u3048\u308b\u5f71\u97ff\u306b\u3064\u3044\u3066\u3001\u3082\u3063\u3068\u5e83\u304f\u8a8d\u8b58\u3055\u308c\u308b\u3088\u3046\u306b\u306a\u3063\u3066\u307b\u3057\u3044\u3002  \u75c5\u6c17\u306e\u9032\u884c\u306e\u53b3\u3057\u3055\u3060\u3051\u3067\u306a\u304f\u3001\u6162\u6027\u75be\u60a3\u3084\u5e0c\u5c11\u75be\u60a3\u306b\u5bfe\u3057\u3066\u3001\u79c1\u305f\u3061\u5168\u54e1\u304c\u3044\u3064\u304b\u306f\u53c2\u52a0\u3057\u306a\u3051\u308c\u3070\u306a\u3089\u306a\u3044\u4fa1\u5024\u3042\u308b\u6226\u3044\u3067\u3042\u308b\u3053\u3068\u3092\u3001\u4ed6\u306e\u4eba\u305f\u3061\u306b\u3082\u7406\u89e3\u3057\u3066\u307b\u3057\u3044\u306e\u3067\u3059\u3002<\/p>\n<p><strong>\u3082\u3057\u660e\u65e5\u3001\u3042\u306a\u305f\u306eLGMD\u304c \"\u6cbb\u308b \"\u3068\u3057\u305f\u3089\u3001\u307e\u305a\u4f55\u3092\u3057\u305f\u3044\u3067\u3059\u304b\uff1f<\/strong>?<\/p>\n<p>\u30c0\u30fc\u30c8\u30d0\u30a4\u30af\u306b\u98db\u3073\u4e57\u3063\u3066\u4f55\u65e5\u3067\u3082\u8d70\u308a\u305f\u3044\uff01  \u82e5\u3044\u9803\u306f\u3088\u304f\u4e57\u3063\u3066\u3044\u305f\u3051\u3069\u3001\u3082\u3046\u4f53\u529b\u304c\u306a\u3044\u3002  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