{"id":2862,"date":"2019-10-01T20:27:15","date_gmt":"2019-10-02T01:27:15","guid":{"rendered":"https:\/\/restruct-lgmd-2021.pantheonsite.io\/?p=2862"},"modified":"2019-10-01T20:27:15","modified_gmt":"2019-10-02T01:27:15","slug":"william","status":"publish","type":"post","link":"https:\/\/www.lgmd-info.org\/ko\/individuals-with-lgmd-interviews\/2019\/10\/01\/william\/","title":{"rendered":"LGMD\uac00 \uc788\ub294 \uac1c\uc778: \uc70c\ub9ac\uc5c4"},"content":{"rendered":"<figure class=\"wp-block-image\"><img decoding=\"async\" src=\"data:image\/svg+xml,%3Csvg%20xmlns%3D%27http%3A%2F%2Fwww.w3.org%2F2000%2Fsvg%27%20width%3D%271024%27%20height%3D%27576%27%20viewBox%3D%270%200%201024%20576%27%3E%3Crect%20width%3D%271024%27%20height%3D%27576%27%20fill-opacity%3D%220%22%2F%3E%3C%2Fsvg%3E\" data-orig-src=\"https:\/\/www.lgmd-info.org\/wp-content\/uploads\/2019\/10\/LGMD1D-William-1024x576.png\" alt=\"\" class=\"lazyload wp-image-2860\"\/><\/figure>\n\n\n\n<p><strong>LGMD \"\uc2a4\ud3ec\ud2b8\ub77c\uc774\ud2b8 \uc778\ud130\ubdf0\"<\/strong><\/p>\n\n\n\n<p><strong>\uc774\ub984<\/strong>:  \uc70c\ub9ac\uc5c4&nbsp;\n<strong>\ub098\uc774<\/strong>:\n62\uc138<\/p>\n\n\n\n<p><strong>\uad6d\uac00<\/strong>: \ubbf8\uad6d<\/p>\n\n\n\n<p><strong>LGMD \ud558\uc704 \uc720\ud615<\/strong>:   LGMD D1 DNAJB6 \uad00\ub828(\uc774\uc804 LGMD 1D\ud615)<\/p>\n\n\n\n<p><strong>\uba87 \uc0b4\uc5d0 \uc9c4\ub2e8\ubc1b\uc73c\uc168\ub098\uc694?<\/strong>:<\/p>\n\n\n\n<p>\uc800\ub294 40\uc138\uc5d0 \uc784\uc0c1 \uc9c4\ub2e8\uc744 \ubc1b\uc558\uace0, 5\ub144 \ud6c4\uc778 45\uc138\uc5d0 \uc720\uc804\uc790 \uac80\uc0ac\ub85c LGMD 1D \uc9c4\ub2e8\uc744 \ubc1b\uc558\uc2b5\ub2c8\ub2e4.<\/p>\n\n\n\n<p><strong>\uccab \uc99d\uc0c1\uc740 \ubb34\uc5c7\uc774\uc5c8\ub098\uc694?<\/strong>:<\/p>\n\n\n\n<p>\uc5b4\ub838\uc744 \ub54c \uc800\ub294 \ub290\ub838\uc5b4\uc694.  45\uc138 \ubb34\ub835\uc5d0\ub294 \ub2ec\ub9ac\uae30\uc5d0 \uc5b4\ub824\uc6c0\uc744 \uacaa\uc5c8\uc2b5\ub2c8\ub2e4.<\/p>\n\n\n\n<p><strong>\ub2e4\ub978 \uac00\uc871 \uc911\uc5d0 LGMD\ub97c \uc553\uace0 \uc788\ub294 \uc0ac\ub78c\uc774 \uc788\ub098\uc694?<\/strong><\/p>\n\n\n\n<p>\ub124, 67\uc138\uc778 \uc81c \ub3d9\uc0dd\ub3c4 LGMD1D\ub97c \uc553\uace0 \uc788\uace0 \uc81c\n\ub538\ub3c4\uc694.<\/p>\n\n\n\n<p><strong>LGMD\uc640 \ud568\uaed8 \uc0dd\ud65c\ud558\uba74\uc11c \uac00\uc7a5 \ud070 \uc5b4\ub824\uc6c0\uc740 \ubb34\uc5c7\uc774\ub77c\uace0 \uc0dd\uac01\ud558\uc2dc\ub098\uc694?\n\uac00\uc7a5 \ud070 \uc5b4\ub824\uc6c0\uc740 \ubb34\uc5c7\uc778\uac00\uc694?<\/strong>:<\/p>\n\n\n\n<p>\uc800\uc5d0\uac8c \uc788\uc5b4 \uac00\uc7a5 \ud070 \ub3c4\uc804 \uacfc\uc81c\ub294\n\uc801\uc751\ud558\uace0 \uc810\ucc28 \uc18d\ub3c4\ub97c \ub2a6\ucd94\ub294 \uac83\uc774\uc5c8\uc2b5\ub2c8\ub2e4.<\/p>\n\n\n\n<p><strong>\uac00\uc7a5 \ud070 \uc131\uacfc\ub294 \ubb34\uc5c7\uc778\uac00\uc694?<\/strong>:<\/p>\n\n\n\n<p>\uac00\uc7a5 \ud070 \uc131\uacfc\ub294 LGMD-1D\n\ube44\uc601\ub9ac \uacf5\uc775 \uc7ac\ub2e8 \uc778 DNAJB6 \uc7ac\ub2e8\uc740 \ub2e4\uc74c\uacfc \uac19\uc740 \uc0ac\uba85\uc744 \uac00\uc9c4 \uc7ac\ub2e8\uc785\ub2c8\ub2e4.\n\uc0ac\uc9c0 \uac70\ub4e4 \uadfc\uc774\uc601\uc591\uc99d 1\ud615(LGMD1D) \uc9c4\ub2e8\uc744 \ubc1b\uc740 \uac1c\uc778\uc744 \uc704\ud55c \uc911\uc2ec\uc801\uc778 \uc704\uce58\ub97c \uc720\uc9c0\ud558\uace0\n\uadfc\uc774\uc601\uc591\uc99d 1D\ud615(LGMD1D) \ud658\uc790\ub4e4\uc744 \ub9cc\ub098\uace0, \uad00\ub828 \ub274\uc2a4\ub97c \ud1b5\ud569\ud558\uace0, \uae30\uae08 \ubaa8\uae08 \ud65c\ub3d9\uc744 \uc2dc\uc791\ud558\uae30 \uc704\ud574\n\uc5f0\uad6c \ubc1c\uc804\uc744 \uc704\ud55c \uae30\uae08 \ubaa8\uae08 \ud65c\ub3d9\uc744 \ud3bc\uce58\uace0 \uc788\uc2b5\ub2c8\ub2e4.&nbsp; <a href=\"https:\/\/lgmd1d.org\">https:\/\/lgmd1d.org<\/a>\n<\/p>\n\n\n\n<p>\ub610\ud55c \uc0c1\uc5fc\uc0c9\uccb4 \uc6b0\uc131 \ud615\ud0dc\uc758 LGMD\ub85c \uc9c4\ub2e8\ubc1b\uc740 \ubaa8\ub4e0 \ud658\uc790\ub97c \uc704\ud55c \ud658\uc790 \ub808\uc9c0\uc2a4\ud2b8\ub9ac\ub97c \uad6c\ucd95\ud588\uc2b5\ub2c8\ub2e4.  (LGMD 1\ud615)<\/p>\n\n\n\n<p><strong>LGMD\uac00 \uc9c0\uae08\uc758 \ub2f9\uc2e0\uc774 \ub418\uae30\uae4c\uc9c0 \uc5b4\ub5a4 \uc601\ud5a5\uc744 \ubbf8\ucce4\ub098\uc694?\n\uc5b4\ub5a4 \uc601\ud5a5\uc744 \ubbf8\ucce4\ub098\uc694?<\/strong><\/p>\n\n\n\n<p>LGMD\ub294 \uc81c \uc0b6\uacfc \uc9c0\uae08\uc758 \uc800\uc5d0\uac8c \uc601\ud5a5\uc744 \ubbf8\ucce4\uc2b5\ub2c8\ub2e4.  \uc18d\ub3c4\ub97c \ub2a6\ucd94\uba74\uc11c \uc81c \uc8fc\ubcc0\uc5d0 \uc788\ub294 \uac83\ub4e4\uc5d0 \uac10\uc0ac\ud558\uac8c \ub418\uc5c8\uc2b5\ub2c8\ub2e4.\n\ub0b4 \uc8fc\ubcc0, \uac00\uc871, \uce5c\uad6c, \uad00\uacc4\uc5d0 \uac10\uc0ac\ud558\uac8c \ub418\uc5c8\uc2b5\ub2c8\ub2e4.<\/p>\n\n\n\n<p><strong>LGMD\uc5d0 \ub300\ud574 \uc804 \uc138\uacc4\uc5d0 \uc54c\ub9ac\uace0 \uc2f6\uc740 \ub0b4\uc6a9<\/strong>:<\/p>\n\n\n\n<p>\uc6b0\ub9ac\ub294 \uce58\ub8cc\ubc95\uc744 \ucc3e\ub294 \ub370 \ub3c4\uc6c0\uc774 \ub418\ub294 \ubc29\uc2dd\uc73c\ub85c \uacc4\uc18d\ud574\uc11c \uc18c\uc2dd\uc744 \uc804\ud558\uace0 \uc5f0\uacb0\ud574\uc57c \ud569\ub2c8\ub2e4.  \uc608\ub97c \ub4e4\uc5b4, \uc0c1\uc5fc\uc0c9\uccb4 \uc6b0\uc131 LGMD(LGMD 1\ud615) \ud658\uc790 \ub4f1\ub85d\uc740 \uce58\ub8cc\ubc95\uc744 \uc5f0\uad6c\ud558\uace0 \ucc3e\ub294 \ub370 \ud544\uc218\uc801\uc785\ub2c8\ub2e4.<\/p>\n\n\n\n<p><strong>\ub9cc\uc57d \ub0b4\uc77c LGMD\uac00 \"\uc644\uce58\"\ub420 \uc218 \uc788\ub2e4\uba74\n\uac00\uc7a5 \uba3c\uc800 \ud558\uace0 \uc2f6\uc740 \uc77c\uc740 \ubb34\uc5c7\uc785\ub2c8\uae4c?<\/strong>:<\/p>\n\n\n\n<p>\ub0b4\uc77c \uc644\uce58\ub418\uba74 \uc190\ub140\ub4e4\uacfc \ucda4\ucd94\uace0 \ucd95\uad6c\ud558\ub7ec \uac08 \uac70\uc608\uc694!!!<\/p>\n\n\n\n<p> <\/p>","protected":false},"excerpt":{"rendered":"<p>LGMD \u201cSpotlight interview\u201d Name:&nbsp; William&nbsp; Age: 62 years old Country: [&hellip;]<\/p>","protected":false},"author":1,"featured_media":2860,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"_acf_changed":false,"footnotes":""},"categories":[13,102,104],"tags":[103],"class_list":["post-2862","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-individuals-with-lgmd-interviews","category-lgmd-d1-dnajb6-related","category-lgmd1d","tag-lgmd-d1-dnajb6-related-united-states-lgmd1d"],"acf":[],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v23.9 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>Individual with LGMD: William - LGMD Awareness Foundation<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/www.lgmd-info.org\/ko\/individuals-with-lgmd-interviews\/2019\/10\/01\/william\/\" \/>\n<meta property=\"og:locale\" content=\"ko_KR\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Individual with LGMD: William - LGMD Awareness Foundation\" \/>\n<meta property=\"og:description\" content=\"LGMD \u201cSpotlight interview\u201d Name:&nbsp; 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