{"id":2716,"date":"2019-04-24T20:13:12","date_gmt":"2019-04-25T01:13:12","guid":{"rendered":"https:\/\/restruct-lgmd-2021.pantheonsite.io\/?p=2716"},"modified":"2021-02-19T18:31:17","modified_gmt":"2021-02-19T18:31:17","slug":"lgmd-researcher-hartzell","status":"publish","type":"post","link":"https:\/\/www.lgmd-info.org\/ru\/lgmd2l\/2019\/04\/24\/lgmd-researcher-hartzell\/","title":{"rendered":"\u0418\u0441\u0441\u043b\u0435\u0434\u043e\u0432\u0430\u0442\u0435\u043b\u044c LGMD: \u0425. \u041a\u0440\u0438\u0441\u0441 \u0425\u0430\u0440\u0442\u0446\u0435\u043b\u043b"},"content":{"rendered":"
\"\"<\/figure>\n

\"LGMD \u0412 \u0426\u0415\u041d\u0422\u0420\u0415 \u0412\u041d\u0418\u041c\u0410\u041d\u0418\u042f - \u0418\u0421\u0421\u041b\u0415\u0414\u041e\u0412\u0410\u041d\u0418\u042f\"<\/strong><\/p>\n

\u0418\u0421\u0421\u041b\u0415\u0414\u041e\u0412\u0410\u0422\u0415\u041b\u042c-\u041f\u0420\u0410\u041a\u0422\u0418\u041a:\u00a0 <\/strong>\u00a0H. \u041a\u0440\u0438\u0441\u0441 \u0425\u0430\u0440\u0442\u0446\u0435\u043b\u043b<\/p>\n

\u041f\u0440\u0438\u043d\u0430\u0434\u043b\u0435\u0436\u043d\u043e\u0441\u0442\u044c:\u00a0 <\/strong>\u041c\u0435\u0434\u0438\u0446\u0438\u043d\u0441\u043a\u0430\u044f \u0448\u043a\u043e\u043b\u0430 \u0423\u043d\u0438\u0432\u0435\u0440\u0441\u0438\u0442\u0435\u0442\u0430 \u042d\u043c\u043e\u0440\u0438<\/p>\n

\u0420\u043e\u043b\u044c \u0438\u043b\u0438 \u0434\u043e\u043b\u0436\u043d\u043e\u0441\u0442\u044c:\u00a0 <\/strong>\u041f\u0440\u043e\u0444\u0435\u0441\u0441\u043e\u0440<\/p>\n

\u041a\u0430\u043a\u043e\u0435 \u043e\u0431\u0440\u0430\u0437\u043e\u0432\u0430\u043d\u0438\u0435 \u0438 \u043f\u043e\u0434\u0433\u043e\u0442\u043e\u0432\u043a\u0443 \u0432\u044b \u043f\u0440\u043e\u0448\u043b\u0438, \u0447\u0442\u043e\u0431\u044b \u0437\u0430\u043d\u044f\u0442\u044c \u0441\u0432\u043e\u044e \u043d\u044b\u043d\u0435\u0448\u043d\u044e\u044e \u0434\u043e\u043b\u0436\u043d\u043e\u0441\u0442\u044c?<\/strong><\/p>\n

\u0423\u043d\u0438\u0432\u0435\u0440\u0441\u0438\u0442\u0435\u0442 \u041b\u043e\u0440\u0435\u043d\u0441\u0430, \u0431\u0430\u043a\u0430\u043b\u0430\u0432\u0440 \u0445\u0438\u043c\u0438\u0438 \u0438 \u0431\u0438\u043e\u043b\u043e\u0433\u0438\u0438<\/p>\n

\u0414\u043e\u043a\u0442\u043e\u0440 \u0444\u0438\u043b\u043e\u0441\u043e\u0444\u0438\u0438 \u0423\u043d\u0438\u0432\u0435\u0440\u0441\u0438\u0442\u0435\u0442\u0430 \u0414\u0436\u043e\u043d\u0430 \u0425\u043e\u043f\u043a\u0438\u043d\u0441\u0430 \u043f\u043e \u0431\u0438\u043e\u043b\u043e\u0433\u0438\u0438.<\/p>\n

\u041f\u043e\u0441\u0442\u0434\u043e\u043a\u0442\u043e\u0440\u0441\u043a\u043e\u0435 \u0438\u0441\u0441\u043b\u0435\u0434\u043e\u0432\u0430\u043d\u0438\u0435 \u0432 \u0413\u0430\u0440\u0432\u0430\u0440\u0434\u0441\u043a\u043e\u0439 \u043c\u0435\u0434\u0438\u0446\u0438\u043d\u0441\u043a\u043e\u0439 \u0448\u043a\u043e\u043b\u0435 \u043d\u0430 \u043a\u0430\u0444\u0435\u0434\u0440\u0435 \u043d\u0435\u0439\u0440\u043e\u0431\u0438\u043e\u043b\u043e\u0433\u0438\u0438<\/p>\n

\u0427\u0442\u043e \u043f\u0440\u0438\u0432\u0435\u043b\u043e \u0432\u0430\u0441 \u043a \u043a\u0430\u0440\u044c\u0435\u0440\u0435 \u0438\u0441\u0441\u043b\u0435\u0434\u043e\u0432\u0430\u0442\u0435\u043b\u044f \u0438, \u0432 \u0447\u0430\u0441\u0442\u043d\u043e\u0441\u0442\u0438, \u043a \u0438\u0437\u0443\u0447\u0435\u043d\u0438\u044e \u043c\u044b\u0448\u0435\u0447\u043d\u043e\u0439 \u0434\u0438\u0441\u0442\u0440\u043e\u0444\u0438\u0438?<\/strong><\/p>\n

\u042f \u0432\u0441\u0435\u0433\u0434\u0430 \u0438\u043d\u0442\u0435\u0440\u0435\u0441\u043e\u0432\u0430\u043b\u0441\u044f \u043d\u0430\u0443\u043a\u043e\u0439, \u0441\u043a\u043e\u043b\u044c\u043a\u043e \u0441\u0435\u0431\u044f \u043f\u043e\u043c\u043d\u044e. \u0412 \u043a\u043e\u043b\u043b\u0435\u0434\u0436\u0435 \u044f \u043f\u0440\u043e\u0447\u0438\u0442\u0430\u043b \u0441\u0442\u0430\u0442\u044c\u044e \u0432 \u0436\u0443\u0440\u043d\u0430\u043b\u0435 Scientific American \u043e \u0442\u0435\u043e\u0440\u0438\u0438 \"\u043f\u0435\u0440\u0435\u043a\u0440\u0435\u0441\u0442\u043d\u043e\u0433\u043e \u043c\u043e\u0441\u0442\u0430\" \u0432 \u0441\u043e\u043a\u0440\u0430\u0449\u0435\u043d\u0438\u0438 \u043c\u044b\u0448\u0446 \u0438 \u0431\u044b\u043b \u043e\u0447\u0430\u0440\u043e\u0432\u0430\u043d \u0438\u0434\u0435\u0435\u0439 \u043e \u0442\u043e\u043c, \u0447\u0442\u043e \u043c\u044b\u0448\u0446\u044b - \u044d\u0442\u043e, \u043f\u043e \u0441\u0443\u0442\u0438, \u043c\u043e\u043b\u0435\u043a\u0443\u043b\u044f\u0440\u043d\u0430\u044f \u043c\u0430\u0448\u0438\u043d\u0430. \u041c\u043e\u044f \u0434\u043e\u043a\u0442\u043e\u0440\u0441\u043a\u0430\u044f \u0440\u0430\u0431\u043e\u0442\u0430 \u0438\u0437\u0443\u0447\u0430\u043b\u0430 \u0430\u0446\u0435\u0442\u0438\u043b\u0445\u043e\u043b\u0438\u043d\u043e\u0432\u044b\u0435 \u0440\u0435\u0446\u0435\u043f\u0442\u043e\u0440\u044b \u043d\u0430 \u043d\u0435\u0440\u0432\u043d\u043e-\u043c\u044b\u0448\u0435\u0447\u043d\u043e\u043c \u0441\u043e\u0435\u0434\u0438\u043d\u0435\u043d\u0438\u0438 \u0438 \u043f\u0440\u0438\u0432\u0435\u043b\u0430 \u043a \u043e\u0442\u043a\u0440\u044b\u0442\u0438\u044e, \u0447\u0442\u043e \u043f\u0440\u0438 \u043c\u0438\u0430\u0441\u0442\u0435\u043d\u0438\u0438 \u0433\u0440\u0430\u0432\u0438\u0441 \u043a\u043e\u043b\u0438\u0447\u0435\u0441\u0442\u0432\u043e \u0430\u0446\u0435\u0442\u0438\u043b\u0445\u043e\u043b\u0438\u043d\u043e\u0432\u044b\u0445 \u0440\u0435\u0446\u0435\u043f\u0442\u043e\u0440\u043e\u0432 \u043d\u0430 \u043d\u0435\u0440\u0432\u043d\u043e-\u043c\u044b\u0448\u0435\u0447\u043d\u043e\u043c \u0441\u043e\u0435\u0434\u0438\u043d\u0435\u043d\u0438\u0438 \u0443\u043c\u0435\u043d\u044c\u0448\u0435\u043d\u043e. \u0412 \u043a\u0430\u0447\u0435\u0441\u0442\u0432\u0435 \u043f\u043e\u0441\u0442\u0434\u043e\u043a\u0430 \u0432 \u0413\u0430\u0440\u0432\u0430\u0440\u0434\u0435 \u044f \u0431\u044b\u043b \u0441\u0442\u0438\u043f\u0435\u043d\u0434\u0438\u0430\u0442\u043e\u043c \u0410\u0441\u0441\u043e\u0446\u0438\u0430\u0446\u0438\u0438 \u043c\u044b\u0448\u0435\u0447\u043d\u043e\u0439 \u0434\u0438\u0441\u0442\u0440\u043e\u0444\u0438\u0438.<\/p>\n

\u041a\u0430\u043a\u0438\u0435 \u0442\u0435\u043c\u044b \u0432\u044b \u0438\u0437\u0443\u0447\u0430\u0435\u0442\u0435?<\/strong><\/p>\n

\u00a0\u041c\u044b \u0438\u0437\u0443\u0447\u0430\u0435\u043c \u0431\u0435\u043b\u043e\u043a ANO5. \u041c\u0443\u0442\u0430\u0446\u0438\u0438 ANO5 \u044f\u0432\u043b\u044f\u044e\u0442\u0441\u044f 4th<\/sup> \u041d\u0430\u0438\u0431\u043e\u043b\u0435\u0435 \u0440\u0430\u0441\u043f\u0440\u043e\u0441\u0442\u0440\u0430\u043d\u0435\u043d\u043d\u0430\u044f \"\u043f\u0440\u0438\u0447\u0438\u043d\u0430\" LGMD, \u043d\u043e \u043f\u043e\u0447\u0442\u0438 \u043d\u0438\u0447\u0435\u0433\u043e \u043d\u0435 \u0438\u0437\u0432\u0435\u0441\u0442\u043d\u043e \u043e \u0442\u043e\u043c, \u0447\u0442\u043e \u0434\u0435\u043b\u0430\u0435\u0442 ANO5 \u0438\u043b\u0438 \u043a\u0430\u043a \u043e\u043d \u0440\u0430\u0431\u043e\u0442\u0430\u0435\u0442. \u041c\u044b \u043f\u043e\u043b\u0430\u0433\u0430\u0435\u043c, \u0447\u0442\u043e \u043e\u043d \u0443\u0447\u0430\u0441\u0442\u0432\u0443\u0435\u0442 \u0432 \u0432\u043e\u0441\u0441\u0442\u0430\u043d\u043e\u0432\u043b\u0435\u043d\u0438\u0438 \u043c\u044b\u0448\u0435\u0447\u043d\u044b\u0445 \u043c\u0435\u043c\u0431\u0440\u0430\u043d. \u041c\u044b \u0438\u0437\u0443\u0447\u0430\u0435\u043c \u044d\u0442\u0443 \u043f\u0440\u043e\u0431\u043b\u0435\u043c\u0443 \u043d\u0430 \u043a\u043b\u0435\u0442\u043e\u0447\u043d\u043e\u043c \u0438 \u043c\u043e\u043b\u0435\u043a\u0443\u043b\u044f\u0440\u043d\u043e\u043c \u0443\u0440\u043e\u0432\u043d\u044f\u0445.<\/p>\n

\u041a\u0430\u043a \u0432\u0430\u0448\u0430 \u0440\u0430\u0431\u043e\u0442\u0430 \u043f\u043e\u043c\u043e\u0436\u0435\u0442 \u043f\u0430\u0446\u0438\u0435\u043d\u0442\u0430\u043c? \u042f\u0432\u043b\u044f\u0435\u0442\u0441\u044f \u043b\u0438 \u043e\u043d\u0430 \u0431\u043e\u043b\u0435\u0435 \u043d\u0430\u0443\u0447\u043d\u043e\u0439 \u043f\u043e \u0441\u0432\u043e\u0435\u0439 \u043f\u0440\u0438\u0440\u043e\u0434\u0435 \u0438\u043b\u0438 \u043c\u043e\u0436\u0435\u0442 \u0441\u0442\u0430\u0442\u044c \u043c\u0435\u0442\u043e\u0434\u043e\u043c \u043b\u0435\u0447\u0435\u043d\u0438\u044f LGMD<\/strong>\u0438\u043b\u0438 MD<\/strong>\u0432 \u0446\u0435\u043b\u043e\u043c?<\/strong><\/p>\n

\u041c\u044b \u0441\u0447\u0438\u0442\u0430\u0435\u043c, \u0447\u0442\u043e \u043f\u043e\u043d\u0438\u043c\u0430\u043d\u0438\u0435 \u043e\u0441\u043d\u043e\u0432 \u043c\u043e\u043b\u0435\u043a\u0443\u043b\u044f\u0440\u043d\u043e\u0439 \u0438 \u043a\u043b\u0435\u0442\u043e\u0447\u043d\u043e\u0439 \u0431\u0438\u043e\u043b\u043e\u0433\u0438\u0438 ANO5 \u044f\u0432\u043b\u044f\u0435\u0442\u0441\u044f \u043d\u0435\u043e\u0431\u0445\u043e\u0434\u0438\u043c\u044b\u043c \u0443\u0441\u043b\u043e\u0432\u0438\u0435\u043c \u0434\u043b\u044f \u0440\u0430\u0437\u0440\u0430\u0431\u043e\u0442\u043a\u0438 \u0442\u0435\u0440\u0430\u043f\u0438\u0438 \u044d\u0442\u043e\u0439 \u0444\u043e\u0440\u043c\u044b LGMD (2L). \u041c\u044b \u0442\u0430\u043a\u0436\u0435 \u0441\u0447\u0438\u0442\u0430\u0435\u043c, \u0447\u0442\u043e \u043f\u043e\u043d\u0438\u043c\u0430\u043d\u0438\u0435 \u0442\u043e\u0433\u043e, \u043a\u0430\u043a \u043f\u0440\u043e\u0438\u0441\u0445\u043e\u0434\u0438\u0442 \u0432\u043e\u0441\u0441\u0442\u0430\u043d\u043e\u0432\u043b\u0435\u043d\u0438\u0435 \u043c\u044b\u0448\u0435\u0447\u043d\u043e\u0439 \u043c\u0435\u043c\u0431\u0440\u0430\u043d\u044b, \u0434\u0430\u0441\u0442 \u043d\u043e\u0432\u044b\u0435 \u043f\u043e\u0434\u0441\u043a\u0430\u0437\u043a\u0438 \u0434\u043b\u044f \u043b\u0435\u0447\u0435\u043d\u0438\u044f \u0434\u0440\u0443\u0433\u0438\u0445 \u0413\u041c\u0414.<\/p>\n

\u0427\u0442\u043e \u0431\u044b \u0432\u044b \u0445\u043e\u0442\u0435\u043b\u0438, \u0447\u0442\u043e\u0431\u044b \u043f\u0430\u0446\u0438\u0435\u043d\u0442\u044b \u0438 \u0434\u0440\u0443\u0433\u0438\u0435 \u043b\u044e\u0434\u0438, \u0438\u043d\u0442\u0435\u0440\u0435\u0441\u0443\u044e\u0449\u0438\u0435\u0441\u044f \u041b\u0413\u041c\u0414, \u0437\u043d\u0430\u043b\u0438 \u043e\u0431 \u0438\u0441\u0441\u043b\u0435\u0434\u043e\u0432\u0430\u043d\u0438\u044f\u0445 (\u0432\u0430\u0448\u0438\u0445 \u0441\u043e\u0431\u0441\u0442\u0432\u0435\u043d\u043d\u044b\u0445 \u043f\u0440\u043e\u0435\u043a\u0442\u0430\u0445 \u0438 \u043e\u0431 \u044d\u0442\u043e\u0439 \u043e\u0431\u043b\u0430\u0441\u0442\u0438 \u0432 \u0446\u0435\u043b\u043e\u043c)?<\/strong><\/p>\n

\u0424\u0443\u043d\u0434\u0430\u043c\u0435\u043d\u0442\u0430\u043b\u044c\u043d\u044b\u0435 \u0438\u0441\u0441\u043b\u0435\u0434\u043e\u0432\u0430\u043d\u0438\u044f \u0438\u0434\u0443\u0442 \u0443\u0434\u0440\u0443\u0447\u0430\u044e\u0449\u0435 \u043c\u0435\u0434\u043b\u0435\u043d\u043d\u043e, \u043f\u043e\u0442\u043e\u043c\u0443 \u0447\u0442\u043e \u043c\u044b \u043d\u0430\u0447\u0438\u043d\u0430\u0435\u043c \u0441 \u0447\u0438\u0441\u0442\u043e\u0433\u043e \u043b\u0438\u0441\u0442\u0430 \u0438 \u0434\u043e\u043b\u0436\u043d\u044b \u0440\u0430\u0437\u0440\u0430\u0431\u043e\u0442\u0430\u0442\u044c \u043d\u043e\u0432\u044b\u0435 \u0438\u043d\u0441\u0442\u0440\u0443\u043c\u0435\u043d\u0442\u044b. \u043d\u043e \u043b\u044e\u0434\u0438 \u0432 \u043c\u043e\u0435\u0439 \u043b\u0430\u0431\u043e\u0440\u0430\u0442\u043e\u0440\u0438\u0438 \u043f\u0440\u0435\u0434\u0430\u043d\u044b \u0441\u0432\u043e\u0435\u043c\u0443 \u0434\u0435\u043b\u0443, \u0440\u0430\u0431\u043e\u0442\u0430\u044e\u0442 \u043f\u043e 12 \u0447\u0430\u0441\u043e\u0432 \u0432 \u0434\u0435\u043d\u044c \u0438 \u0440\u0435\u0434\u043a\u043e \u043f\u0435\u0440\u0435\u0441\u0442\u0430\u044e\u0442 \u0434\u0443\u043c\u0430\u0442\u044c \u0438 \u0431\u0435\u0441\u043f\u043e\u043a\u043e\u0438\u0442\u044c\u0441\u044f \u043e \u0442\u043e\u043c, \u043a\u0430\u043a \u0440\u0435\u0448\u0438\u0442\u044c \u0432\u043e\u043f\u0440\u043e\u0441\u044b, \u043d\u0430 \u043a\u043e\u0442\u043e\u0440\u044b\u0435 \u043c\u044b \u0445\u043e\u0442\u0438\u043c \u043f\u043e\u043b\u0443\u0447\u0438\u0442\u044c \u043e\u0442\u0432\u0435\u0442\u044b. \u043c\u044b \u0446\u0435\u043d\u0438\u043c \u043f\u043e\u0434\u0434\u0435\u0440\u0436\u043a\u0443 \u043d\u0430\u043b\u043e\u0433\u043e\u043f\u043b\u0430\u0442\u0435\u043b\u044c\u0449\u0438\u043a\u043e\u0432 \u0438 \u0434\u043e\u043d\u043e\u0440\u043e\u0432, \u043a\u043e\u0442\u043e\u0440\u044b\u0435 \u0444\u0438\u043d\u0430\u043d\u0441\u0438\u0440\u0443\u044e\u0442 \u043d\u0430\u0448\u0438 \u0438\u0441\u0441\u043b\u0435\u0434\u043e\u0432\u0430\u043d\u0438\u044f.<\/p>\n

\u0427\u0442\u043e \u0432\u0434\u043e\u0445\u043d\u043e\u0432\u043b\u044f\u0435\u0442 \u0432\u0430\u0441 \u043f\u0440\u043e\u0434\u043e\u043b\u0436\u0430\u0442\u044c \u0440\u0430\u0431\u043e\u0442\u0430\u0442\u044c \u0432 \u044d\u0442\u043e\u0439 \u043e\u0431\u043b\u0430\u0441\u0442\u0438? <\/strong><\/p>\n

\u0423 \u043c\u0435\u043d\u044f \u043d\u0430\u0432\u044f\u0437\u0447\u0438\u0432\u044b\u0439\/\u043a\u043e\u043c\u043f\u0443\u043b\u044c\u0441\u0438\u0432\u043d\u044b\u0439 \u0445\u0430\u0440\u0430\u043a\u0442\u0435\u0440, \u0438 \u044f \u043d\u0435 \u043c\u043e\u0433\u0443 \u0443\u0441\u043f\u043e\u043a\u043e\u0438\u0442\u044c\u0441\u044f, \u043f\u043e\u043a\u0430 \u043d\u0435 \u043f\u043e\u0439\u043c\u0443, \u043a\u0430\u043a \u0432\u0441\u0435 \u0443\u0441\u0442\u0440\u043e\u0435\u043d\u043e. \u041c\u0435\u043d\u044f \u0432\u0434\u043e\u0445\u043d\u043e\u0432\u043b\u044f\u044e\u0442 \u043b\u044e\u0434\u0438, \u0441\u0442\u0440\u0430\u0434\u0430\u044e\u0449\u0438\u0435 \u044d\u0442\u0438\u043c\u0438 \u0437\u0430\u0431\u043e\u043b\u0435\u0432\u0430\u043d\u0438\u044f\u043c\u0438, \u043a\u043e\u0442\u043e\u0440\u044b\u0435 \u043f\u043e\u0434\u0434\u0435\u0440\u0436\u0438\u0432\u0430\u044e\u0442 \u0441\u0432\u043e\u0438\u0445 \u043f\u0430\u0446\u0438\u0435\u043d\u0442\u043e\u0432 \u0438 \u0440\u0430\u0431\u043e\u0442\u0430\u044e\u0442 \u043d\u0430\u0434 \u043e\u0431\u044a\u0435\u0434\u0438\u043d\u0435\u043d\u0438\u0435\u043c \u0441\u043e\u043e\u0431\u0449\u0435\u0441\u0442\u0432\u0430 LGMD.<\/p>\n

\u041a\u0430\u043a \u043f\u0430\u0446\u0438\u0435\u043d\u0442\u044b \u043c\u043e\u0433\u0443\u0442 \u043f\u043e\u043e\u0449\u0440\u044f\u0442\u044c \u0432\u0430\u0441 \u0438 \u043f\u043e\u043c\u043e\u0433\u0430\u0442\u044c \u0432\u0430\u0448\u0435\u0439 \u0440\u0430\u0431\u043e\u0442\u0435?<\/strong><\/p>\n

\u00a0\u041e\u0434\u043d\u043e \u0438\u0437 \u0433\u043b\u0430\u0432\u043d\u044b\u0445 \u043f\u0440\u0435\u043f\u044f\u0442\u0441\u0442\u0432\u0438\u0439, \u0441 \u043a\u043e\u0442\u043e\u0440\u044b\u043c \u043c\u044b \u0441\u0442\u0430\u043b\u043a\u0438\u0432\u0430\u0435\u043c\u0441\u044f \u0432 \u043d\u0430\u0448\u0438\u0445 \u0438\u0441\u0441\u043b\u0435\u0434\u043e\u0432\u0430\u043d\u0438\u044f\u0445, - \u0434\u043e\u0441\u0442\u0443\u043f \u043a \u0447\u0435\u043b\u043e\u0432\u0435\u0447\u0435\u0441\u043a\u0438\u043c \u0442\u043a\u0430\u043d\u044f\u043c. \u0425\u043e\u0442\u044f \u043c\u044b \u043c\u043e\u0436\u0435\u043c \u043c\u043d\u043e\u0433\u043e\u0435 \u0443\u0437\u043d\u0430\u0442\u044c, \u0438\u0441\u043f\u043e\u043b\u044c\u0437\u0443\u044f \u043c\u043e\u0434\u0435\u043b\u0438 \u043c\u044b\u0448\u0435\u0439 \u0438 \u043a\u043b\u0435\u0442\u043e\u0447\u043d\u044b\u0445 \u043a\u0443\u043b\u044c\u0442\u0443\u0440, \u0434\u043b\u044f \u043f\u043e\u043d\u0438\u043c\u0430\u043d\u0438\u044f \u0431\u043e\u043b\u0435\u0437\u043d\u0438 \u0447\u0435\u043b\u043e\u0432\u0435\u043a\u0430 \u043d\u0435\u043e\u0431\u0445\u043e\u0434\u0438\u043c\u043e \u0438\u0441\u043f\u043e\u043b\u044c\u0437\u043e\u0432\u0430\u0442\u044c \u0447\u0435\u043b\u043e\u0432\u0435\u0447\u0435\u0441\u043a\u0438\u0435 \u0442\u043a\u0430\u043d\u0438. \u041f\u0430\u0446\u0438\u0435\u043d\u0442\u044b, \u0433\u043e\u0442\u043e\u0432\u044b\u0435 \u043f\u0440\u0435\u0434\u043e\u0441\u0442\u0430\u0432\u0438\u0442\u044c \u0431\u0438\u043e\u043f\u0441\u0438\u044e \u0438 \u043b\u0438\u0447\u043d\u044b\u0435 \u043d\u0430\u0431\u043b\u044e\u0434\u0435\u043d\u0438\u044f \u0437\u0430 \u0440\u0430\u0437\u0432\u0438\u0442\u0438\u0435\u043c \u0431\u043e\u043b\u0435\u0437\u043d\u0438, \u0432\u043d\u043e\u0441\u044f\u0442 \u043e\u0433\u0440\u043e\u043c\u043d\u044b\u0439 \u0432\u043a\u043b\u0430\u0434 \u0432 \u043d\u0430\u0448\u0443 \u0438\u0441\u0441\u043b\u0435\u0434\u043e\u0432\u0430\u0442\u0435\u043b\u044c\u0441\u043a\u0443\u044e \u043f\u0440\u043e\u0433\u0440\u0430\u043c\u043c\u0443.<\/p>\n<\/div><\/div><\/div><\/div><\/div>","protected":false},"excerpt":{"rendered":"","protected":false},"author":1,"featured_media":4258,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"_acf_changed":false,"footnotes":""},"categories":[91,49,92],"tags":[],"class_list":["post-2716","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-researcher-interview","category-lgmd2l","category-researcher"],"acf":[],"yoast_head":"\nLGMD RESEARCHER: H. Criss Hartzell - LGMD Awareness Foundation<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/www.lgmd-info.org\/ru\/lgmd2l\/2019\/04\/24\/lgmd-researcher-hartzell\/\" \/>\n<meta property=\"og:locale\" content=\"ru_RU\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"LGMD RESEARCHER: H. Criss Hartzell - LGMD Awareness Foundation\" \/>\n<meta property=\"og:url\" content=\"https:\/\/www.lgmd-info.org\/ru\/lgmd2l\/2019\/04\/24\/lgmd-researcher-hartzell\/\" \/>\n<meta property=\"og:site_name\" content=\"LGMD Awareness Foundation\" \/>\n<meta property=\"article:publisher\" content=\"https:\/\/www.facebook.com\/LGMDawareness\/\" \/>\n<meta property=\"article:published_time\" content=\"2019-04-25T01:13:12+00:00\" \/>\n<meta property=\"article:modified_time\" content=\"2021-02-19T18:31:17+00:00\" \/>\n<meta property=\"og:image\" content=\"https:\/\/www.lgmd-info.org\/wp-content\/uploads\/2019\/04\/Hartzell-Criss.png\" \/>\n\t<meta property=\"og:image:width\" content=\"960\" \/>\n\t<meta property=\"og:image:height\" content=\"720\" \/>\n\t<meta property=\"og:image:type\" content=\"image\/png\" \/>\n<meta name=\"author\" content=\"dooley\" \/>\n<meta name=\"twitter:card\" content=\"summary_large_image\" \/>\n<meta name=\"twitter:creator\" content=\"@LgmdAwareness\" \/>\n<meta name=\"twitter:site\" content=\"@LgmdAwareness\" \/>\n<meta name=\"twitter:label1\" content=\"Written by\" \/>\n\t<meta name=\"twitter:data1\" content=\"dooley\" \/>\n\t<meta name=\"twitter:label2\" content=\"Est. reading time\" \/>\n\t<meta name=\"twitter:data2\" content=\"3 minutes\" \/>\n<script type=\"application\/ld+json\" class=\"yoast-schema-graph\">{\"@context\":\"https:\/\/schema.org\",\"@graph\":[{\"@type\":\"Article\",\"@id\":\"https:\/\/www.lgmd-info.org\/tr\/lgmd2l\/2019\/04\/24\/lgmd-researcher-hartzell\/#article\",\"isPartOf\":{\"@id\":\"https:\/\/www.lgmd-info.org\/tr\/lgmd2l\/2019\/04\/24\/lgmd-researcher-hartzell\/\"},\"author\":{\"name\":\"dooley\",\"@id\":\"https:\/\/www.lgmd-info.org\/de\/#\/schema\/person\/007755074875959ad5503c1c969678c7\"},\"headline\":\"LGMD RESEARCHER: H. Criss Hartzell\",\"datePublished\":\"2019-04-25T01:13:12+00:00\",\"dateModified\":\"2021-02-19T18:31:17+00:00\",\"mainEntityOfPage\":{\"@id\":\"https:\/\/www.lgmd-info.org\/tr\/lgmd2l\/2019\/04\/24\/lgmd-researcher-hartzell\/\"},\"wordCount\":656,\"publisher\":{\"@id\":\"https:\/\/www.lgmd-info.org\/de\/#organization\"},\"image\":{\"@id\":\"https:\/\/www.lgmd-info.org\/tr\/lgmd2l\/2019\/04\/24\/lgmd-researcher-hartzell\/#primaryimage\"},\"thumbnailUrl\":\"https:\/\/www.lgmd-info.org\/wp-content\/uploads\/2019\/04\/Hartzell-Criss.png\",\"articleSection\":[\"LGMD Researcher - Interviews\",\"LGMD2L\",\"RESEARCHER\"],\"inLanguage\":\"ru-RU\"},{\"@type\":\"WebPage\",\"@id\":\"https:\/\/www.lgmd-info.org\/tr\/lgmd2l\/2019\/04\/24\/lgmd-researcher-hartzell\/\",\"url\":\"https:\/\/www.lgmd-info.org\/tr\/lgmd2l\/2019\/04\/24\/lgmd-researcher-hartzell\/\",\"name\":\"LGMD RESEARCHER: H. Criss Hartzell - LGMD Awareness Foundation\",\"isPartOf\":{\"@id\":\"https:\/\/www.lgmd-info.org\/de\/#website\"},\"primaryImageOfPage\":{\"@id\":\"https:\/\/www.lgmd-info.org\/tr\/lgmd2l\/2019\/04\/24\/lgmd-researcher-hartzell\/#primaryimage\"},\"image\":{\"@id\":\"https:\/\/www.lgmd-info.org\/tr\/lgmd2l\/2019\/04\/24\/lgmd-researcher-hartzell\/#primaryimage\"},\"thumbnailUrl\":\"https:\/\/www.lgmd-info.org\/wp-content\/uploads\/2019\/04\/Hartzell-Criss.png\",\"datePublished\":\"2019-04-25T01:13:12+00:00\",\"dateModified\":\"2021-02-19T18:31:17+00:00\",\"breadcrumb\":{\"@id\":\"https:\/\/www.lgmd-info.org\/tr\/lgmd2l\/2019\/04\/24\/lgmd-researcher-hartzell\/#breadcrumb\"},\"inLanguage\":\"ru-RU\",\"potentialAction\":[{\"@type\":\"ReadAction\",\"target\":[\"https:\/\/www.lgmd-info.org\/tr\/lgmd2l\/2019\/04\/24\/lgmd-researcher-hartzell\/\"]}]},{\"@type\":\"ImageObject\",\"inLanguage\":\"ru-RU\",\"@id\":\"https:\/\/www.lgmd-info.org\/tr\/lgmd2l\/2019\/04\/24\/lgmd-researcher-hartzell\/#primaryimage\",\"url\":\"https:\/\/www.lgmd-info.org\/wp-content\/uploads\/2019\/04\/Hartzell-Criss.png\",\"contentUrl\":\"https:\/\/www.lgmd-info.org\/wp-content\/uploads\/2019\/04\/Hartzell-Criss.png\",\"width\":960,\"height\":720,\"caption\":\"Hartzell Criss\"},{\"@type\":\"BreadcrumbList\",\"@id\":\"https:\/\/www.lgmd-info.org\/tr\/lgmd2l\/2019\/04\/24\/lgmd-researcher-hartzell\/#breadcrumb\",\"itemListElement\":[{\"@type\":\"ListItem\",\"position\":1,\"name\":\"Home\",\"item\":\"https:\/\/www.lgmd-info.org\/de\/\"},{\"@type\":\"ListItem\",\"position\":2,\"name\":\"LGMD RESEARCHER: H. Criss Hartzell\"}]},{\"@type\":\"WebSite\",\"@id\":\"https:\/\/www.lgmd-info.org\/de\/#website\",\"url\":\"https:\/\/www.lgmd-info.org\/de\/\",\"name\":\"LGMD Awareness Foundation\",\"description\":\"Information Hub for the LGMD community\",\"publisher\":{\"@id\":\"https:\/\/www.lgmd-info.org\/de\/#organization\"},\"potentialAction\":[{\"@type\":\"SearchAction\",\"target\":{\"@type\":\"EntryPoint\",\"urlTemplate\":\"https:\/\/www.lgmd-info.org\/de\/?s={search_term_string}\"},\"query-input\":{\"@type\":\"PropertyValueSpecification\",\"valueRequired\":true,\"valueName\":\"search_term_string\"}}],\"inLanguage\":\"ru-RU\"},{\"@type\":\"Organization\",\"@id\":\"https:\/\/www.lgmd-info.org\/de\/#organization\",\"name\":\"LGMD Awareness Foundation, Inc.\",\"url\":\"https:\/\/www.lgmd-info.org\/de\/\",\"logo\":{\"@type\":\"ImageObject\",\"inLanguage\":\"ru-RU\",\"@id\":\"https:\/\/www.lgmd-info.org\/de\/#\/schema\/logo\/image\/\",\"url\":\"https:\/\/lgmd-info.org\/wp-content\/uploads\/2021\/02\/LGMD_Logo.png\",\"contentUrl\":\"https:\/\/lgmd-info.org\/wp-content\/uploads\/2021\/02\/LGMD_Logo.png\",\"width\":208,\"height\":61,\"caption\":\"LGMD Awareness Foundation, Inc.\"},\"image\":{\"@id\":\"https:\/\/www.lgmd-info.org\/de\/#\/schema\/logo\/image\/\"},\"sameAs\":[\"https:\/\/www.facebook.com\/LGMDawareness\/\",\"https:\/\/x.com\/LgmdAwareness\",\"https:\/\/www.instagram.com\/lgmdawareness\/\"]},{\"@type\":\"Person\",\"@id\":\"https:\/\/www.lgmd-info.org\/de\/#\/schema\/person\/007755074875959ad5503c1c969678c7\",\"name\":\"dooley\",\"image\":{\"@type\":\"ImageObject\",\"inLanguage\":\"ru-RU\",\"@id\":\"https:\/\/www.lgmd-info.org\/de\/#\/schema\/person\/image\/\",\"url\":\"https:\/\/secure.gravatar.com\/avatar\/c87b3b784fd4c1975884b6c3eab282b5?s=96&d=mm&r=g\",\"contentUrl\":\"https:\/\/secure.gravatar.com\/avatar\/c87b3b784fd4c1975884b6c3eab282b5?s=96&d=mm&r=g\",\"caption\":\"dooley\"},\"sameAs\":[\"https:\/\/live-lgmd-2021.pantheonsite.io\"]}]}<\/script>\n<!-- \/ Yoast SEO plugin. -->","yoast_head_json":{"title":"LGMD RESEARCHER: H. Criss Hartzell - LGMD Awareness Foundation","robots":{"index":"index","follow":"follow","max-snippet":"max-snippet:-1","max-image-preview":"max-image-preview:large","max-video-preview":"max-video-preview:-1"},"canonical":"https:\/\/www.lgmd-info.org\/ru\/lgmd2l\/2019\/04\/24\/lgmd-researcher-hartzell\/","og_locale":"ru_RU","og_type":"article","og_title":"LGMD RESEARCHER: H. Criss Hartzell - LGMD Awareness Foundation","og_url":"https:\/\/www.lgmd-info.org\/ru\/lgmd2l\/2019\/04\/24\/lgmd-researcher-hartzell\/","og_site_name":"LGMD Awareness Foundation","article_publisher":"https:\/\/www.facebook.com\/LGMDawareness\/","article_published_time":"2019-04-25T01:13:12+00:00","article_modified_time":"2021-02-19T18:31:17+00:00","og_image":[{"width":960,"height":720,"url":"https:\/\/www.lgmd-info.org\/wp-content\/uploads\/2019\/04\/Hartzell-Criss.png","type":"image\/png"}],"author":"dooley","twitter_card":"summary_large_image","twitter_creator":"@LgmdAwareness","twitter_site":"@LgmdAwareness","twitter_misc":{"Written by":"dooley","Est. reading time":"3 minutes"},"schema":{"@context":"https:\/\/schema.org","@graph":[{"@type":"Article","@id":"https:\/\/www.lgmd-info.org\/tr\/lgmd2l\/2019\/04\/24\/lgmd-researcher-hartzell\/#article","isPartOf":{"@id":"https:\/\/www.lgmd-info.org\/tr\/lgmd2l\/2019\/04\/24\/lgmd-researcher-hartzell\/"},"author":{"name":"dooley","@id":"https:\/\/www.lgmd-info.org\/de\/#\/schema\/person\/007755074875959ad5503c1c969678c7"},"headline":"LGMD RESEARCHER: H. Criss Hartzell","datePublished":"2019-04-25T01:13:12+00:00","dateModified":"2021-02-19T18:31:17+00:00","mainEntityOfPage":{"@id":"https:\/\/www.lgmd-info.org\/tr\/lgmd2l\/2019\/04\/24\/lgmd-researcher-hartzell\/"},"wordCount":656,"publisher":{"@id":"https:\/\/www.lgmd-info.org\/de\/#organization"},"image":{"@id":"https:\/\/www.lgmd-info.org\/tr\/lgmd2l\/2019\/04\/24\/lgmd-researcher-hartzell\/#primaryimage"},"thumbnailUrl":"https:\/\/www.lgmd-info.org\/wp-content\/uploads\/2019\/04\/Hartzell-Criss.png","articleSection":["LGMD Researcher - Interviews","LGMD2L","RESEARCHER"],"inLanguage":"ru-RU"},{"@type":"WebPage","@id":"https:\/\/www.lgmd-info.org\/tr\/lgmd2l\/2019\/04\/24\/lgmd-researcher-hartzell\/","url":"https:\/\/www.lgmd-info.org\/tr\/lgmd2l\/2019\/04\/24\/lgmd-researcher-hartzell\/","name":"LGMD RESEARCHER: H. Criss Hartzell - LGMD Awareness Foundation","isPartOf":{"@id":"https:\/\/www.lgmd-info.org\/de\/#website"},"primaryImageOfPage":{"@id":"https:\/\/www.lgmd-info.org\/tr\/lgmd2l\/2019\/04\/24\/lgmd-researcher-hartzell\/#primaryimage"},"image":{"@id":"https:\/\/www.lgmd-info.org\/tr\/lgmd2l\/2019\/04\/24\/lgmd-researcher-hartzell\/#primaryimage"},"thumbnailUrl":"https:\/\/www.lgmd-info.org\/wp-content\/uploads\/2019\/04\/Hartzell-Criss.png","datePublished":"2019-04-25T01:13:12+00:00","dateModified":"2021-02-19T18:31:17+00:00","breadcrumb":{"@id":"https:\/\/www.lgmd-info.org\/tr\/lgmd2l\/2019\/04\/24\/lgmd-researcher-hartzell\/#breadcrumb"},"inLanguage":"ru-RU","potentialAction":[{"@type":"ReadAction","target":["https:\/\/www.lgmd-info.org\/tr\/lgmd2l\/2019\/04\/24\/lgmd-researcher-hartzell\/"]}]},{"@type":"ImageObject","inLanguage":"ru-RU","@id":"https:\/\/www.lgmd-info.org\/tr\/lgmd2l\/2019\/04\/24\/lgmd-researcher-hartzell\/#primaryimage","url":"https:\/\/www.lgmd-info.org\/wp-content\/uploads\/2019\/04\/Hartzell-Criss.png","contentUrl":"https:\/\/www.lgmd-info.org\/wp-content\/uploads\/2019\/04\/Hartzell-Criss.png","width":960,"height":720,"caption":"Hartzell Criss"},{"@type":"BreadcrumbList","@id":"https:\/\/www.lgmd-info.org\/tr\/lgmd2l\/2019\/04\/24\/lgmd-researcher-hartzell\/#breadcrumb","itemListElement":[{"@type":"ListItem","position":1,"name":"Home","item":"https:\/\/www.lgmd-info.org\/de\/"},{"@type":"ListItem","position":2,"name":"LGMD RESEARCHER: H. Criss Hartzell"}]},{"@type":"WebSite","@id":"https:\/\/www.lgmd-info.org\/de\/#website","url":"https:\/\/www.lgmd-info.org\/de\/","name":"LGMD Awareness Foundation","description":"Information Hub for the LGMD community","publisher":{"@id":"https:\/\/www.lgmd-info.org\/de\/#organization"},"potentialAction":[{"@type":"SearchAction","target":{"@type":"EntryPoint","urlTemplate":"https:\/\/www.lgmd-info.org\/de\/?s={search_term_string}"},"query-input":{"@type":"PropertyValueSpecification","valueRequired":true,"valueName":"search_term_string"}}],"inLanguage":"ru-RU"},{"@type":"Organization","@id":"https:\/\/www.lgmd-info.org\/de\/#organization","name":"LGMD Awareness Foundation, Inc.","url":"https:\/\/www.lgmd-info.org\/de\/","logo":{"@type":"ImageObject","inLanguage":"ru-RU","@id":"https:\/\/www.lgmd-info.org\/de\/#\/schema\/logo\/image\/","url":"https:\/\/lgmd-info.org\/wp-content\/uploads\/2021\/02\/LGMD_Logo.png","contentUrl":"https:\/\/lgmd-info.org\/wp-content\/uploads\/2021\/02\/LGMD_Logo.png","width":208,"height":61,"caption":"LGMD Awareness Foundation, Inc."},"image":{"@id":"https:\/\/www.lgmd-info.org\/de\/#\/schema\/logo\/image\/"},"sameAs":["https:\/\/www.facebook.com\/LGMDawareness\/","https:\/\/x.com\/LgmdAwareness","https:\/\/www.instagram.com\/lgmdawareness\/"]},{"@type":"Person","@id":"https:\/\/www.lgmd-info.org\/de\/#\/schema\/person\/007755074875959ad5503c1c969678c7","name":"dooley","image":{"@type":"ImageObject","inLanguage":"ru-RU","@id":"https:\/\/www.lgmd-info.org\/de\/#\/schema\/person\/image\/","url":"https:\/\/secure.gravatar.com\/avatar\/c87b3b784fd4c1975884b6c3eab282b5?s=96&d=mm&r=g","contentUrl":"https:\/\/secure.gravatar.com\/avatar\/c87b3b784fd4c1975884b6c3eab282b5?s=96&d=mm&r=g","caption":"dooley"},"sameAs":["https:\/\/live-lgmd-2021.pantheonsite.io"]}]}},"_links":{"self":[{"href":"https:\/\/www.lgmd-info.org\/ru\/wp-json\/wp\/v2\/posts\/2716","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/www.lgmd-info.org\/ru\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/www.lgmd-info.org\/ru\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/www.lgmd-info.org\/ru\/wp-json\/wp\/v2\/users\/1"}],"replies":[{"embeddable":true,"href":"https:\/\/www.lgmd-info.org\/ru\/wp-json\/wp\/v2\/comments?post=2716"}],"version-history":[{"count":1,"href":"https:\/\/www.lgmd-info.org\/ru\/wp-json\/wp\/v2\/posts\/2716\/revisions"}],"predecessor-version":[{"id":4523,"href":"https:\/\/www.lgmd-info.org\/ru\/wp-json\/wp\/v2\/posts\/2716\/revisions\/4523"}],"wp:featuredmedia":[{"embeddable":true,"href":"https:\/\/www.lgmd-info.org\/ru\/wp-json\/wp\/v2\/media\/4258"}],"wp:attachment":[{"href":"https:\/\/www.lgmd-info.org\/ru\/wp-json\/wp\/v2\/media?parent=2716"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/www.lgmd-info.org\/ru\/wp-json\/wp\/v2\/categories?post=2716"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/www.lgmd-info.org\/ru\/wp-json\/wp\/v2\/tags?post=2716"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}