{"id":2109,"date":"2018-07-20T09:14:56","date_gmt":"2018-07-20T14:14:56","guid":{"rendered":"https:\/\/restruct-lgmd-2021.pantheonsite.io\/?p=2109"},"modified":"2018-07-20T09:14:56","modified_gmt":"2018-07-20T14:14:56","slug":"lgmd-researcher-emerson","status":"publish","type":"post","link":"https:\/\/www.lgmd-info.org\/zh\/researcher-interview\/2018\/07\/20\/lgmd-researcher-emerson\/","title":{"rendered":"LGMD \u7814\u7a76\u5458\uff1aCharles P. Emerson, Jr., Ph.D."},"content":{"rendered":"<p>LGMD \"\u7814\u7a76\u805a\u7126\u8bbf\u8c08\"<\/p>\n<p><span style=\"color: #000000;\"><strong>lgmd \u7814\u7a76\u5458\uff1a<\/strong> Charles P. Emerson, Jr., Ph.D.<a style=\"color: #000000;\" href=\"https:\/\/www.lgmd-info.org\/wp-content\/uploads\/2018\/07\/Emerson-Charles.png\"><img decoding=\"async\" class=\"lazyload size-medium wp-image-2108 alignright\" src=\"data:image\/svg+xml,%3Csvg%20xmlns%3D%27http%3A%2F%2Fwww.w3.org%2F2000%2Fsvg%27%20width%3D%27300%27%20height%3D%27225%27%20viewBox%3D%270%200%20300%20225%27%3E%3Crect%20width%3D%27300%27%20height%3D%27225%27%20fill-opacity%3D%220%22%2F%3E%3C%2Fsvg%3E\" data-orig-src=\"https:\/\/www.lgmd-info.org\/wp-content\/uploads\/2018\/07\/Emerson-Charles-300x225.png\" alt=\"\" width=\"300\" height=\"225\" \/><\/a><\/span><\/p>\n<p><span style=\"color: #000000;\"><strong>\u6240\u5c5e\u5355\u4f4d\uff1a\u00a0 <\/strong>\u795e\u7ecf\u75c5\u5b66\u6559\u6388\uff1bUMMS Wellstone \u808c\u8089\u840e\u7f29\u75c7\u9879\u76ee\u4e3b\u4efb<\/span><\/p>\n<p>&nbsp;<\/p>\n<p><span style=\"color: #000000;\"><strong>\u60a8\u63a5\u53d7\u8fc7\u54ea\u4e9b\u6559\u80b2\u548c\u57f9\u8bad\u624d\u80fd\u62c5\u4efb\u76ee\u524d\u7684\u804c\u4f4d\uff1f<\/strong><\/span><\/p>\n<p><span style=\"color: #000000;\">\u6211\u7684\u672c\u79d1\u4e13\u4e1a\u662f\u751f\u7269\/\u751f\u7269\u5316\u5b66\uff0c\u5176\u4e2d\u5305\u62ec\u4e09\u4e2a\u6691\u5047\u7684\u808c\u8089\u86cb\u767d\u8d28\u751f\u7269\u5316\u5b66\u7814\u7a76\u3002 <\/span>\u9886\u5bfc<span style=\"color: #000000;\"> \u6211\u7684\u7814\u7a76\u751f\u5b66\u4f4d\u548c\u7814\u7a76\u57f9\u8bad\u8ba9\u6211\u4ece\u4e8b\u751f\u7269\u533b\u5b66\u7814\u7a76\u5de5\u4f5c\uff0c\u8fd9\u9879\u5de5\u4f5c\u81f3\u4eca\u4ecd\u8ba9\u6211\u5174\u594b\u4e0d\u5df2\u3002\u6211\u7684\u7814\u7a76\u751f\u5b66\u4f4d\u548c\u7814\u7a76\u57f9\u8bad <\/span>\u662f<span style=\"color: #000000;\"> \u5206\u5b50\u548c\u7ec6\u80de\u751f\u7269\u5b66\u65b0\u5174\u9886\u57df\uff0c\u91cd\u70b9\u662f <\/span>\u5e94\u7528<span style=\"color: #000000;\"> \u6211\u7684\u535a\u58eb\u540e\u7814\u7a76\u8bfe\u9898\u662f\u4ee5\u53d1\u80b2\u4e2d\u7684\u6d77\u80c6\u80da\u80ce\u4e3a\u6a21\u578b\u7cfb\u7edf\uff0c\u7814\u7a76\u53d1\u80b2\u57fa\u56e0\u8c03\u63a7\u673a\u5236\u7684\u5206\u5b50\u751f\u7269\u5b66\u65b9\u6cd5\u3002\u6211\u7684\u535a\u58eb\u540e\u57f9\u8bad\u5c06\u6211\u672c\u79d1\u65f6\u5bf9\u808c\u8089\u751f\u7269\u5b66\u7684\u5174\u8da3\u548c\u7814\u7a76\u751f\u65f6\u5bf9\u53d1\u80b2\u57fa\u56e0\u8c03\u63a7\u7684\u5174\u8da3\u7ed3\u5408\u5728\u4e00\u8d77\uff0c\u5f00\u59cb\u4e86\u6211\u5bf9\u53d1\u80b2\u57fa\u56e0\u8c03\u63a7\u673a\u5236\u7684\u7814\u7a76\u3002 <\/span>\u7ec8\u8eab<span style=\"color: #000000;\"> \u6211\u7684\u7814\u7a76\u5386\u7a0b\u662f\u5229\u7528\u591a\u79cd\u751f\u7269\u7cfb\u7edf\uff0c\u5305\u62ec\u808c\u8089\u7ec6\u80de\u57f9\u517b\u548c\u679c\u8747\u3001\u9e1f\u7c7b\u548c\u5c0f\u9f20\u9057\u4f20\u548c\u80da\u80ce\u52a8\u7269\u6a21\u578b\uff0c\u4ee5\u53ca\u7ec6\u80de\u4fe1\u53f7\u3001\u57fa\u56e0\u514b\u9686\u548c DNA \u6d4b\u5e8f\u3001\u8f6c\u5f55\u8c03\u63a7\u548c\u7ec6\u80de\u91cd\u7f16\u7a0b\u7b49\u5b9e\u9a8c\u65b9\u6cd5\uff0c\u7814\u7a76\u808c\u8089\u53d1\u80b2\u548c\u5206\u5316\u7684\u57fa\u672c\u673a\u5236\u3002\u5927\u7ea6\u5341\u5e74\u524d\uff0c\u6211\u53d7\u5230\u542f\u53d1\uff0c\u5c06\u7814\u7a76\u65b9\u5411\u5b8c\u5168\u8f6c\u5411\u4eba\u7c7b\u808c\u8089\u53d1\u80b2\u548c\u808c\u8089\u840e\u7f29\u75c7\u3002<\/span><\/p>\n<p>&nbsp;<\/p>\n<p><span style=\"color: #000000;\"><strong>\u662f\u4ec0\u4e48\u4fc3\u4f7f\u60a8\u4ece\u4e8b\u7814\u7a76\u5de5\u4f5c\uff0c\u5c24\u5176\u662f\u7814\u7a76\u808c\u8089\u840e\u7f29\u75c7\uff1f<\/strong><\/span><\/p>\n<p><span style=\"color: #000000;\">10 \u5e74\u524d\uff0c\u6211\u7684\u7814\u7a76\u4e3b\u8981\u96c6\u4e2d\u5728\u4e86\u89e3\u80da\u80ce\u7ec6\u80de\u57fa\u56e0\u7ec4\u7684\u57fa\u56e0\u8c03\u63a7\u673a\u5236\u3002 <\/span>\u53d8\u6210<span style=\"color: #000000;\"> \u808c\u8089\u5e72\u7ec6\u80de\u5728\u5206\u5316\u8fc7\u7a0b\u4e2d\u8868\u8fbe\u808c\u8089\u57fa\u56e0\u3002\u6211\u7684\u7814\u7a76\u5f97\u5230\u4e86\u7f8e\u56fd\u56fd\u7acb\u536b\u751f\u7814\u7a76\u9662\uff08NIH\uff09\u548c\u808c\u8089\u840e\u7f29\u75c7\u534f\u4f1a\uff08Muscular Dystrophy Association\uff09\u7684\u6177\u6168\u652f\u6301\u3002\u6211\u51b3\u5b9a\u5c06\u6211\u7684\u7814\u7a76\u8ba1\u5212\u91cd\u65b0\u805a\u7126\u4e8e\u4eba\u7c7b\u808c\u8089\u751f\u7269\u5b66\u548c\u75be\u75c5\uff0c\u90e8\u5206\u539f\u56e0\u662f\u7075\u611f\uff0c\u90e8\u5206\u539f\u56e0\u662f\u8ba4\u8bc6\u5230\u65f6\u673a\u5df2\u7ecf\u6210\u719f\u3002 <\/span>\u6765<span style=\"color: #000000;\"> \u5229\u7528\u6211\u7684\u57fa\u7840\u79d1\u5b66\u4e13\u4e1a\u77e5\u8bc6\u505a\u51fa\u8d21\u732e\u3002\u9996\u5148\u662f\u7075\u611f\u3002\u8fd9\u6e90\u4e8e\u6211\u4e0e\u80a2\u4f53\u6b8b\u75be\u4eba\u58eb\u548c\u5bb6\u5ead\u7684\u4e2a\u4eba\u8054\u7cfb\u3002\u6211\u7684\u5973\u513f\u56e0\u51fa\u751f\u65f6\u8111\u90e8\u53d7\u4f24\u800c\u5bfc\u81f4\u4e25\u91cd\u80a2\u4f53\u6b8b\u75be\u3002\u6211\u5bf9\u5979\u7684\u52c7\u6c14\u548c\u51b3\u5fc3\u8868\u793a\u611f\u8c22\uff0c\u6700\u8fd1\u53d1\u660e\u7684\u7535\u52a8\u8f6e\u6905\u548c\u7535\u8111\u4e3a\u5979\u63d0\u4f9b\u4e86\u6781\u5927\u7684\u4fbf\u5229\uff0c\u8ba9\u5979\u8fc7\u4e0a\u4e86\u6709\u610f\u4e49\u7684\u751f\u6d3b\u3002\u6211\u7684\u5973\u513f\u4e00\u76f4\u5728\u63d0\u9192\u6211\uff0c\u6211\u5728\u808c\u8089\u751f\u7269\u5b66\u65b9\u9762\u7684\u4e13\u4e1a\u77e5\u8bc6\u4e5f\u8bb8\u6709\u4e00\u5929\u80fd\u591f <\/span>\u5e2e\u52a9<span style=\"color: #000000;\"> \u6709\u808c\u8089\u6b8b\u75be\u7684\u513f\u7ae5\u548c\u6210\u4eba\uff0c\u5e76\u6b23\u8d4f <\/span>\u770b\u4f3c\u5fae\u5c0f\u7684\u6539\u8fdb<span style=\"color: #000000;\"> \u808c\u8089\u529f\u80fd\u969c\u788d\u4f1a\u5bf9\u80a2\u4f53\u6b8b\u75be\u4eba\u7684\u751f\u6d3b\u8d28\u91cf\u4ea7\u751f\u5de8\u5927\u5f71\u54cd\u3002\u5341\u5e74\u524d\u7684\u4e00\u4e2a\u4e0b\u5348\uff0c\u4e00\u4f4d\u60a3\u6709\u808c\u8089\u840e\u7f29\u75c7\u7684\u4e39\u5c3c\u5c14-\u4f69\u96f7\u65af\u6765\u5230\u6211\u7684\u529e\u516c\u5ba4\u3002 <\/span>\u5b9e\u9a8c\u5ba4<span style=\"color: #000000;\"> \u4ed6\u5750\u5728\u8f6e\u6905\u4e0a\u95ee\u6211\uff0c\u4e3a\u4ec0\u4e48\u6211\u8fd9\u4e2a\u4f18\u79c0\u7684\u808c\u8089\u751f\u7269\u5b66\u5bb6\u4e0d\u7814\u7a76\u4ed6\u7684\u808c\u8089\u75be\u75c5\u3002\u6211\u4ece\u6765\u6ca1\u542c\u8bf4\u8fc7\u4ed6\u7684\u75c5--FSHD\uff0c\u8fd9\u8ba9\u6211\u5927\u5403\u4e00\u60ca\uff0c\u5c3d\u7ba1\u6211\u6709 \"\u808c\u8089\u65b9\u9762\u7684\u4e13\u4e1a\u77e5\u8bc6\"\uff0c\u4f46\u6211\u5bf9\u4efb\u4f55\u4e00\u79cd\u808c\u8089\u840e\u7f29\u75c7\u51e0\u4e4e\u4e00\u65e0\u6240\u77e5\u3002  \u4e39\u5c3c\u5c14\u4e3a\u6211\u6253\u5f00\u4e86\u4e00\u6247\u901a\u5f80\u808c\u8089\u840e\u7f29\u75c7\u7814\u7a76\u4e16\u754c\u7684\u5927\u95e8\u3002\u4ed6\u5bf9\u524d\u5217\u817a\u589e\u751f\u75c7\u548c\u808c\u8089\u840e\u7f29\u75c7\u7684\u7814\u7a76\u975e\u5e38\u4e86\u89e3\uff0c\u4ed6\u6b63\u5728\u5efa\u7acb\u548c\u6559\u80b2\u4e00\u4e2a\u7531\u9876\u5c16\u808c\u8089\u7814\u7a76\u4eba\u5458\u7ec4\u6210\u7684\u7f51\u7edc\uff0c\u4ee5\u8c03\u67e5\u808c\u8089\u840e\u7f29\u75c7\u5e76\u786e\u5b9a\u5177\u4f53\u7684\u7814\u7a76\u91cd\u70b9\uff0c\u4ed6\u8fd8\u79ef\u6781\u6709\u6548\u5730\u5411\u56fd\u4f1a\u5021\u5bfc\u7f8e\u56fd\u56fd\u7acb\u536b\u751f\u7814\u7a76\u9662\uff08NIH\uff09\u63d0\u4f9b\u8d44\u91d1\uff0c\u5e76\u7ec4\u7ec7\u524d\u5217\u817a\u589e\u751f\u75c7\u60a3\u8005\u548c\u5bb6\u5c5e\u53c2\u4e0e\u7814\u7a76\u3002  \u6211\u8fd8\u610f\u8bc6\u5230\uff0c\u901a\u8fc7\u6211\u5728\u808c\u8089\u5e72\u7ec6\u80de\u751f\u7269\u5b66\u548c\u57fa\u56e0\u8c03\u63a7\u65b9\u9762\u7684\u4e13\u4e1a\u77e5\u8bc6\uff0c\u5c06\u6211\u7684\u808c\u8089\u57fa\u7840\u79d1\u5b66\u8f6c\u5316\u4e3a\u4eba\u7c7b\u808c\u8089\u75be\u75c5\u6a21\u578b\u7684\u65f6\u673a\u5df2\u7ecf\u6210\u719f\uff0c\u8fd9\u4e9b\u4e13\u4e1a\u77e5\u8bc6\u4f7f\u6211\u80fd\u591f\u5f00\u53d1 FSHD \u548c\u73b0\u5728\u7684 LGMDs \u808c\u8089\u8425\u517b\u4e0d\u826f\u75c7\u7684\u4eba\u7c7b\u7ec6\u80de\u6a21\u578b\uff0c\u4ece\u800c\u5bf9\u7279\u5b9a\u8425\u517b\u4e0d\u826f\u75c7\u7684\u5206\u5b50\u75c5\u7406\u5b66\u6709\u4e86\u65b0\u7684\u8ba4\u8bc6\uff0c\u5e76\u4e3a\u5229\u7528\u60a3\u8005\u808c\u8089\u5f00\u53d1\u6cbb\u7597\u836f\u7269\u63d0\u4f9b\u4e86\u5b9e\u9a8c\u5e73\u53f0\uff0c\u8fdc\u8fdc\u8d85\u8d8a\u4e86\u52a8\u7269\u75be\u75c5\u6a21\u578b\u3002\u5728\u8fc7\u53bb\u7684 10 \u5e74\u4e2d\uff0c\u6211\u7684\u7814\u7a76\u5b8c\u5168\u91cd\u65b0\u805a\u7126\u4e8e\u4eba\u7c7b\u808c\u8089\u751f\u7269\u5b66\u548c\u808c\u8089\u8425\u517b\u4e0d\u826f\u75c7\uff0c\u6700\u521d\u662f\u524d\u72b6\u808c\u8425\u517b\u4e0d\u826f\u75c7\uff0c\u6700\u8fd1\u662f\u5305\u62ec LGMD2i \u548c 2G \u5728\u5185\u7684 LGMDs\u3002\u4e0e\u524d\u5217\u817a\u589e\u751f\u75c7\u4e00\u6837\uff0c\u6211\u5bf9 LGMDs \u7684\u7814\u7a76\u4e5f\u53d7\u5230\u4e86\u60a3\u8005\u548c\u5021\u5bfc\u8005\u7684\u542f\u53d1\uff0c\u4ed6\u4eec\u5145\u6ee1\u70ed\u60c5\uff0c\u4e86\u89e3\u60c5\u51b5\uff0c\u5e76\u5e0c\u671b\u80fd\u5728\u4ed6\u4eec\u7684\u75be\u75c5\u4e2d\u627e\u5230\u6cbb\u7597\u65b9\u6cd5\u3002 <\/span>\u5c81\u6708<span style=\"color: #000000;\">.<\/span><\/p>\n<p>&nbsp;<\/p>\n<p><span style=\"color: #000000;\"><strong>\u60a8\u6b63\u5728\u7814\u7a76\u54ea\u4e9b\u8bfe\u9898\uff1f<\/strong><\/span><\/p>\n<p><span style=\"color: #000000;\">\u5982\u4eca\uff0c\u6211\u7684\u7814\u7a76\u5b9e\u9a8c\u5ba4\u6b63\u4e0e\u4e00\u6279\u624d\u534e\u6a2a\u6ea2\u3001\u901a\u529b\u5408\u4f5c\u7684\u5b66\u672f\u754c\u548c\u4ea7\u4e1a\u754c\u5408\u4f5c\u4f19\u4f34\u3001\u4e34\u5e8a\u533b\u751f\u548c\u60a3\u8005\u4e00\u8d77\uff0c\u81f4\u529b\u4e8e\u836f\u7269\u3001\u5e72\u7ec6\u80de\u548c\u57fa\u56e0\u77eb\u6b63\u7597\u6cd5\u7684\u4e34\u5e8a\u524d\u5f00\u53d1\u548c\u9a8c\u8bc1\uff0c\u4ee5\u6cbb\u7597\u524d\u5217\u817a\u589e\u751f\u75c7\u3001LGMD2i <\/span>\u548c<span style=\"color: #000000;\"> LGMD2G.<\/span><\/p>\n<p>&nbsp;<\/p>\n<p><span style=\"color: #000000;\"><strong>\u60a8\u7684\u5de5\u4f5c\u5c06\u5982\u4f55\u5e2e\u52a9\u75c5\u4eba\uff1f\u5b83\u7684\u79d1\u5b66\u6027\u66f4\u5f3a\uff0c\u8fd8\u662f\u53ef\u80fd\u6210\u4e3a LGMD \u6216\u4e00\u822c\u533b\u5b66\u535a\u58eb\u7684\u6cbb\u7597\u65b9\u6cd5\uff1f<\/strong><\/span><\/p>\n<p><span style=\"color: #000000;\">\u6211\u4e4b\u6240\u4ee5\u80fd\u591f\u5f00\u5c55\u808c\u8089\u840e\u7f29\u75c7\u7597\u6cd5\u7684\u7814\u7a76\uff0c\u662f\u56e0\u4e3a\u60a3\u8005\u548c\u5bb6\u5c5e\u70ed\u5fc3\u5730\u5c06\u4ed6\u4eec\u7684\u7ec6\u80de\u548c\u808c\u8089\u7ec4\u7ec7\u6350\u732e\u7ed9\u6211\u8fd9\u6837\u7684\u7814\u7a76\u4eba\u5458\uff0c\u4f7f\u6211\u4eec\u80fd\u591f\u5f00\u53d1\u836f\u7269\u3001\u5e72\u7ec6\u80de\u548c\u57fa\u56e0\u77eb\u6b63\u5de5\u5177\u4ee5\u53ca\u75be\u75c5\u751f\u7269\u6807\u5fd7\u7269\uff0c\u4ee5\u4e86\u89e3\u4eba\u7c7b\u75be\u75c5\u7684\u75c5\u7406\uff0c\u652f\u6301\u672a\u6765\u7684\u4e34\u5e8a\u8bd5\u9a8c\uff0c\u800c\u8fd9\u662f\u4f7f\u7528\u4eba\u7c7b\u75be\u75c5\u52a8\u7269\u6a21\u578b\u65e0\u6cd5\u5b9e\u73b0\u7684\u3002\u6211\u4eec\u7684\u76ee\u6807 <\/span>\u53d1\u5c55<span style=\"color: #000000;\"> \u9488\u5bf9 FSHD\u3001LGMD2i \u548c LGMD2G 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href=\"https:\/\/www.lgmd-info.org\/zh\/\">https:\/\/www.lgmd-info.org\/<\/a><\/p>","protected":false},"excerpt":{"rendered":"<p>LGMD \u201cSpotlight Interview on Research\u201d LGMD RESEARCHER: Charles P. Emerson, [&hellip;]<\/p>","protected":false},"author":1,"featured_media":2108,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"_acf_changed":false,"footnotes":""},"categories":[91,92],"tags":[],"class_list":["post-2109","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-researcher-interview","category-researcher"],"acf":[],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v23.9 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>LGMD RESEARCHER: Charles P. 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