{"id":7663,"date":"2023-04-22T16:20:29","date_gmt":"2023-04-22T16:20:29","guid":{"rendered":"https:\/\/restruct-lgmd-2021.pantheonsite.io\/?p=7663"},"modified":"2024-02-09T14:23:48","modified_gmt":"2024-02-09T14:23:48","slug":"peter","status":"publish","type":"post","link":"https:\/\/www.lgmd-info.org\/zh\/lgmd2c\/2023\/04\/22\/peter\/","title":{"rendered":"\u60a3\u6709 LGMD \u7684\u4e2a\u4eba\uff1a \u5f7c\u5f97"},"content":{"rendered":"<div class=\"fusion-fullwidth fullwidth-box fusion-builder-row-1 fusion-flex-container nonhundred-percent-fullwidth non-hundred-percent-height-scrolling\" style=\"--awb-border-radius-top-left:0px;--awb-border-radius-top-right:0px;--awb-border-radius-bottom-right:0px;--awb-border-radius-bottom-left:0px;--awb-flex-wrap:wrap;\" ><div class=\"fusion-builder-row fusion-row fusion-flex-align-items-flex-start fusion-flex-content-wrap\" style=\"max-width:1456px;margin-left: calc(-4% \/ 2 );margin-right: calc(-4% \/ 2 );\"><div class=\"fusion-layout-column fusion_builder_column fusion-builder-column-0 fusion_builder_column_1_1 1_1 fusion-flex-column\" style=\"--awb-bg-size:cover;--awb-width-large:100%;--awb-margin-top-large:0px;--awb-spacing-right-large:1.92%;--awb-margin-bottom-large:0px;--awb-spacing-left-large:1.92%;--awb-width-medium:100%;--awb-spacing-right-medium:1.92%;--awb-spacing-left-medium:1.92%;--awb-width-small:100%;--awb-spacing-right-small:1.92%;--awb-spacing-left-small:1.92%;\"><div class=\"fusion-column-wrapper fusion-flex-justify-content-flex-start fusion-content-layout-column\"><div class=\"fusion-text fusion-text-1\"><p><img decoding=\"async\" class=\"lazyload aligncenter size-medium wp-image-6116\" src=\"data:image\/svg+xml,%3Csvg%20xmlns%3D%27http%3A%2F%2Fwww.w3.org%2F2000%2Fsvg%27%20width%3D%27300%27%20height%3D%27169%27%20viewBox%3D%270%200%20300%20169%27%3E%3Crect%20width%3D%27300%27%20height%3D%27169%27%20fill-opacity%3D%220%22%2F%3E%3C%2Fsvg%3E\" data-orig-src=\"https:\/\/www.lgmd-info.org\/wp-content\/uploads\/2023\/04\/LGMD2C-Peter-300x169.png\" alt=\"Lgmd2c Peter\" width=\"300\" height=\"169\" \/><\/p>\n<p><strong>\u540d\u79f0<\/strong>:  \u5f7c\u5f97<\/p>\n<p><strong>\u5e74\u9f84<\/strong>: \u00a010<\/p>\n<p><strong>\u56fd\u5bb6<\/strong>:  \u7f8e\u56fd<\/p>\n<p><strong>LGMD \u5b50\u7c7b\u578b<\/strong>:  LGMD 2C\/R5 \u03b3-\u808c\u7cd6\u86cb\u767d\u75c5<\/p>\n<p><em>* \u7531\u5f7c\u5f97\u7684\u6bcd\u4eb2\u5b8c\u6210<\/em><\/p>\n<p><strong>\u60a8\u5728\u51e0\u5c81\u65f6\u88ab\u786e\u8bca<\/strong>?<\/p>\n<p>\u6211 9 \u5c81\u65f6\u88ab\u8bca\u65ad\u51fa\u60a3\u6709\u808c\u8089\u65e0\u529b\u75c7\u3002\u7238\u5988\u5f00\u59cb\u6ce8\u610f\u5230\u808c\u8089\u65e0\u529b\u7684\u60c5\u51b5\u8d8a\u6765\u8d8a\u4e25\u91cd\uff0c\u8fd9\u8ba9\u4ed6\u4eec\u975e\u5e38\u62c5\u5fc3\uff0c\u4e8e\u662f\u6211\u4eec\u5e26\u5f7c\u5f97\u53bb\u521d\u7ea7\u4fdd\u5065\u533b\u751f\u90a3\u91cc\u5316\u9a8c\uff0c\u68c0\u67e5\u662f\u5426\u60a3\u6709\u795e\u7ecf\u808c\u8089\u75be\u75c5\u3002\u6211\u4eec\u53d1\u73b0\u808c\u9178\u6fc0\u9176\u5347\u9ad8\uff0c\u4e8e\u662f\u5f00\u59cb\u4e86\u8bca\u65ad\u4e4b\u65c5--\u57fa\u56e0\u68c0\u6d4b\u8bc1\u5b9e\u4e86 LGMD 2C\u3002<\/p>\n<p><strong>\u60a8\u6700\u521d\u7684\u75c7\u72b6\u662f\u4ec0\u4e48\uff1f <\/strong><\/p>\n<p>6-7 \u5c81\u65f6\u51fa\u73b0\u7684\u65e9\u671f\u75c7\u72b6\u5305\u62ec\u5c0f\u817f\u80a5\u5927\u3001\u8f7b\u5fae\u7528\u811a\u5c16\u8d70\u8def\uff0c\u4ee5\u53ca\u5728\u4e0e\u5e74\u9f84\u76f8\u9002\u5e94\u7684\u8fd0\u52a8\u4e2d\u8ddf\u4e0d\u4e0a\u540c\u9f84\u4eba\u7684\u6b65\u4f10\uff08\u5982\u8dd1\u5792\u3001\u51fb\u6253\u68d2\u7403\u7b49\uff09\u3002<\/p>\n<p>8-9 \u5c81\u65f6\u7684\u75c7\u72b6\u5305\u62ec\uff1a\u4ece\u5730\u677f\u4e0a\u7ad9\u8d77\u6765\u65f6\u5f88\u96be\u7528\u817f\u7ad9\u8d77\u6765\uff0c\u4e0a\u697c\u68af\u56f0\u96be\uff0c\u7ecf\u5e38\u6454\u5012\u3002<\/p>\n<p><strong>\u60a8\u6709\u5176\u4ed6\u5bb6\u5ead\u6210\u5458\u60a3\u6709 LGMD \u5417\uff1f<\/strong><\/p>\n<p>\u59b9\u59b9 7 \u5c81\uff0c\u540e\u6765\u88ab\u8bca\u65ad\u4e3a LGMD 2C\u3002\u7236\u6bcd\u6216\u5bb6\u65cf\u6210\u5458\u5747\u65e0\u4efb\u4f55\u8425\u517b\u4e0d\u826f\u75c5\u53f2\u3002<\/p>\n<p><strong>\u60a8\u8ba4\u4e3a LGMD \u60a3\u8005\u5728\u751f\u6d3b\u4e2d\u9762\u4e34\u7684\u6700\u5927\u6311\u6218\u662f\u4ec0\u4e48\uff1f<\/strong>?<\/p>\n<p>\u5f7c\u5f97\u5728\u4e00\u5929\u7684\u5b66\u4e60\u751f\u6d3b\u4e2d\u5f00\u59cb\u8868\u73b0\u51fa\u4e00\u4e9b\u75b2\u60eb\uff0c\u9700\u8981\u7ecf\u5e38\u4f11\u606f\uff0c\u9700\u8981\u989d\u5916\u7684\u65f6\u95f4\u53bb\u4e0a\u8bfe\uff0c\u5728\u8bfe\u5802\u4e0a\u4e5f\u9700\u8981\u4e00\u4e9b\u7167\u987e\u3002\u722c\u697c\u68af\u548c\u8fdc\u8ddd\u79bb\u884c\u8d70\u7684\u56f0\u96be\u51e0\u4e4e\u6bcf\u5929\u90fd\u662f\u4e00\u4e2a\u6311\u6218\u3002<\/p>\n<p><strong>\u60a8\u6700\u5927\u7684\u6210\u5c31\u662f\u4ec0\u4e48\uff1f<\/strong><\/p>\n<p>\u5c3d\u7ba1\u88ab\u6392\u9664\u5728\u8fd0\u52a8\u961f\u4e4b\u5916\uff0c\u6709\u65f6\u4e5f\u8ddf\u4e0d\u4e0a\u540c\u5b66\u4eec\u7684\u8282\u594f\uff0c\u4f46\u5f7c\u5f97\u5728\u6574\u4e2a\u5c0f\u5b66\u671f\u95f4\u90fd\u5efa\u7acb\u4e86\u7f8e\u597d\u7684\u53cb\u8c0a\u3002\u5f53\u4ed6\u5f00\u59cb\u51fa\u73b0\u75c7\u72b6\u65f6\uff0c\u4ed6\u7684\u670b\u53cb\u4eec\u90fd\u56e2\u7ed3\u5728\u4ed6\u5468\u56f4\uff0c\u652f\u6301\u548c\u5e2e\u52a9\u4ed6\u3002\u4e8b\u5b9e\u4e0a\uff0c\u4ed6\u7684\u5927\u591a\u6570\u670b\u53cb\u90fd\u79f0\u5f7c\u5f97\u662f\u4ed6\u4eec\u7684 \"\u6700\u597d\u7684\u670b\u53cb\"\u3002<\/p>\n<p><strong>LGMD \u662f\u5982\u4f55\u5f71\u54cd\u60a8\u6210\u4e3a\u4eca\u5929\u7684\u81ea\u5df1\u7684\uff1f<\/strong><\/p>\n<p>\u5f7c\u5f97\u4ecd\u5728\u5b66\u4e60\u6709\u5173 LGMD \u7684\u77e5\u8bc6\u3002\u6211\u4eec\u7528\u9002\u5408\u4ed6\u5e74\u9f84\u7684\u8bed\u8a00\u8ba8\u8bba\u4e86\u4ed6\u7684\u795e\u7ecf\u808c\u8089\u75be\u75c5\uff0c\u540c\u65f6\u5bf9\u4e00\u4e2a 10 \u5c81\u5b69\u5b50 \"\u8c37\u6b4c \"\u4efb\u4f55\u4e1c\u897f\u7684\u80fd\u529b\u6301\u8c28\u614e\u6001\u5ea6\u3002\u6211\u4eec\u8ba8\u8bba\u4e86\u7269\u7406\u6cbb\u7597\u3001\u4f38\u5c55\u8fd0\u52a8\u548c\u75b2\u52b3\u65f6\u4f11\u606f\u7684\u91cd\u8981\u6027\u3002\u5728\u8fc7\u53bb\u7684\u51e0\u5e74\u91cc\uff0c\u5f7c\u5f97\u4e00\u76f4\u5728\u52aa\u529b\u575a\u6301\uff0c\u6ca1\u6709\u62b1\u6028\u4e5f\u6ca1\u6709\u653e\u5f03\uff0c\u800c\u4ed6\u6240\u4ed8\u51fa\u7684\u52aa\u529b\u8fdc\u8fdc\u8d85\u51fa\u4e86\u6211\u4eec\u7684\u8ba4\u77e5\u3002\u5f7c\u5f97\u5bf9\u98de\u673a\u3001\u822a\u7a7a\u6bcd\u8230\u3001\u6d77\u519b\u8230\u8247\u7b49\u5de5\u7a0b\u548c\u5efa\u7b51\u5f88\u611f\u5174\u8da3\u3002\u4ed6\u7684\u68a6\u60f3\u662f\u8bbe\u8ba1\u548c\u5efa\u9020\u6d77\u519b\u8230\u8247\uff0c\u5982\u822a\u7a7a\u6bcd\u8230\u548c\u9a71\u9010\u8230\u3002<\/p>\n<p><strong>\u60a8\u5e0c\u671b\u4e16\u754c\u4e86\u89e3 LGMD \u7684\u54ea\u4e9b\u65b9\u9762\uff1f<\/strong>?<\/p>\n<p>\u4f5c\u4e3a\u4e00\u4e2a\u5bb6\u5ead\uff0c\u6211\u4eec\u5e0c\u671b\u63d0\u9ad8\u4eba\u4eec\u5bf9 LGMD \u7684\u8ba4\u8bc6\uff0c\u7279\u522b\u662f\u5bf9\u808c\u7518\u9178\u75c7\u7684\u8ba4\u8bc6\u3002\u8fd9\u4e9b\u9057\u4f20\u3001\u7f55\u89c1\u7684\u57fa\u56e0\u75be\u75c5\u53ef\u80fd\u5728\u6ca1\u6709\u4efb\u4f55\u5f81\u5146\u6216\u5bb6\u65cf\u53f2\u7684\u60c5\u51b5\u4e0b\u53d1\u751f\u3002\u5bf9 LGMD \u7684\u7814\u7a76\u6709\u9650\uff0c\u6f5c\u5728\u7684\u6cbb\u7597\u65b9\u6848\u4e5f\u6709\u9650\u3002\u5173\u4e8e LGMD \u7684\u4e00\u4e2a\u5e38\u89c1\u8bef\u89e3\u662f\uff0c\u5b83\u53ef\u80fd\u5728\u665a\u5e74\u53d1\u751f\uff0c\u800c\u4e14 \"\u8fdb\u5c55\u7f13\u6162\"--\u7136\u800c\uff0c\u808c\u7403\u86cb\u767d\u75c7\u901a\u5e38\u4f1a\u5f71\u54cd\u513f\u7ae5\uff0c\u800c\u4e14\u75be\u75c5\u8fdb\u5c55\u8fc5\u901f\u3002<\/p>\n<p><strong>\u5982\u679c\u60a8\u7684 LGMD \u660e\u5929\u5c31\u80fd 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